Investigative Magnetic Resonance Imaging

Korean Society of Magnetic Resonance in Medicine (대한자기공명의과학회)
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MRI Findings of Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA syndrome) with a Blind Megaureter: Case Report

  • Cho, Yun Hee (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Sung, Deuk Jae (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Han, Na Yeon (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Park, Beom Jin (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Kim, Min Ju (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Sim, Ki Choon (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University) ;
  • Cho, Sung Bum (Department of Radiology, Korea University Anam Hospital, College of Medicine, Korea University)
  • Received : 2015.07.19
  • Accepted : 2015.08.27
  • Published : 2015.09.30
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Abstract

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is an uncommon congenital abnormality of the female urogenital tract characterized by the triad of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. A 13-year-old female presented with acute lower abdominal pain. Magnetic resonance imaging (MRI) revealed uterine didelphys, hematometrocolpos, obstructed hemivagina, and right ipsilateral agenesis, consistent with OHVIRA syndrome. Also, a well-defined mass with fluid signal intensity, mimicking adnexal neoplasm was seen in the right lower pelvic cavity adjacent to the posterior wall of the bladder. Vaginal septotomy and drainage of hematometrocolpos were done initially, but unilateral hysterectomy was later performed to relieve the patient's symptoms. The cystic mass in the right lower pelvic cavity was also excised and confirmed as a blind megaureter.

Keywords

References

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  1. Two Cases of Herlyn-Werner-Wunderlich Syndrome in Neonates and Adolescents with Hydrocolpos and Hematocolpometra vol.30, pp.4, 2015, https://doi.org/10.14734/pn.2019.30.4.236