Journal of Yeungnam Medical Science
- Volume 32 Issue 2
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- Pages.114-117
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- 2015
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- 2799-8010(eISSN)
DOI QR Code
Rosai-Dorfman disease of soft tissue
연부조직에 발생한 로사이-돌프만 병
- Song, Seung Eon (Department of Internal Medicine, Dae Dong Hospital) ;
- Lim, Tae Won (Department of Internal Medicine, Dae Dong Hospital) ;
- Lee, Kwang Jae (Department of Internal Medicine, Dae Dong Hospital) ;
- Jo, A Ra (Department of Internal Medicine, Dae Dong Hospital) ;
- Chae, Byung Do (Department of General Surgery, Dae Dong Hospital) ;
- Ko, Myung Ju (Department of Pathology, Dae Dong Hospital) ;
- Lee, Chae Won (Department of Pathology, Dae Dong Hospital)
- 송승언 (대동병원 내과) ;
- 임태원 (대동병원 내과) ;
- 이광재 (대동병원 내과) ;
- 조아라 (대동병원 내과) ;
- 채병도 (대동병원 외과) ;
- 고명주 (대동병원 병리과) ;
- 이채원 (대동병원 병리과)
- Received : 2014.07.17
- Accepted : 2014.08.25
- Published : 2015.12.31
Abstract
Rosai-Dorfman disease (RDD) is a benign proliferative histiocytic disorder of unknown etiology, which typically manifests as lymphadenopathy and systemic symptoms. Lymph node involvement is typical, but soft tissue RDD without nodal or systemic involvement is extremely rare. We report on a case of soft tissue RDD in a 16-year-old girl with a palpable mass on her buttock. It was firm, mobile, and discrete without tenderness. Excisional biopsy was performed, then RDD was confirmed histologically. RDD is a non-neo-plastic disease that should be considered in the differential diagnosis of other soft tissue tumors. While the optimal treatment for extranodal RDD remains controversial, surgical excision is typically curative.