The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Sick Sinus Syndrome in a Patient with Systemic Sclerosis

전신경화증 환자에서 발생한 동기능부전증후군 1예

  • Kim, Dong Hyun (Department of Internal Medicine, Chosun University School of Medicine) ;
  • Kim, Sung Jung (Department of Internal Medicine, Chosun University School of Medicine) ;
  • So, Jung Hae (Department of Internal Medicine, Chosun University School of Medicine) ;
  • Lim, Gyun Seop (Department of Internal Medicine, Chosun University School of Medicine) ;
  • Kim, Hyung Ho (Department of Internal Medicine, Chosun University School of Medicine) ;
  • Kim, Hyun-Sook (Department of Internal Medicine, Sunchunhyang University College of Medicine) ;
  • Kim, Yun Sung (Department of Internal Medicine, Chosun University School of Medicine)
  • 김동현 (조선대학교 의학전문대학원 내과학교실) ;
  • 김성중 (조선대학교 의학전문대학원 내과학교실) ;
  • 소중해 (조선대학교 의학전문대학원 내과학교실) ;
  • 임균섭 (조선대학교 의학전문대학원 내과학교실) ;
  • 김형호 (조선대학교 의학전문대학원 내과학교실) ;
  • 김현숙 (순천향대학교 의학전문대학원 내과학교실) ;
  • 김윤성 (조선대학교 의학전문대학원 내과학교실)
  • Received : 2013.04.12
  • Accepted : 2013.08.05
  • Published : 2014.01.01
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Abstract

Systemic sclerosis (SSc) is characterized by the presence of microvascular disease and various patterns of cutaneous and parenchymal fibrosis. Manifestation of SSc may occur in numerous tissues and organs and can be particularly problematic when present in the lungs, kidneys or heart. Cardiac involvement in SSc includes pericarditis, myocardial disease, conduction abnormalities, and arrhythmia. Sick sinus syndrome is described as a combination of symptoms (dizziness, confusion, fatigue, syncope and congestive heart failure) caused by sinus node dysfunction and manifested by marked sinus bradycardia, sinoatrial block, or sinus arrest. Sinus node dysfunction is most often seen in the elderly but also, rarely, in systemic amyloidosis and connective tissue disease. Sick sinus syndrome is rarely found in patients with SSc, of which there has been only one case report, according to a review of the literature. Therefore, we report a case of sick sinus syndrome in a 71-year-old female with SSc.

Keywords

Acknowledgement

Supported by : Chosun University

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