The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Recovered Atrioventricular Conduction in Behçet Disease after Immunotherapy

베체트병 환자에서 면역억제치료 후 방실전도장애가 호전된 1예

  • Kim, Seong Yoon (Korea Association of Health Promotion, Western Seoul Branch) ;
  • Shin, Seung Yong (Division of Cardiology, Department of Internal Medicine, Armed Forces Capital Hospital) ;
  • Yang, Ji Hyun (Division of Cardiology, Department of Internal Medicine, Armed Forces Capital Hospital) ;
  • Woo, Jong Shin (Division of Cardiology, Department of Internal Medicine, Armed Forces Capital Hospital) ;
  • Kim, Duk-Kyung (Division of Cardiology, Department of Medicine, Cardiac and Vascular Center, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Cha, Hoon-Suk (Division of Rheumatology, Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Kim, Sung-Soon (Division of Cardiology, Department of Internal Medicine, Armed Forces Capital Hospital)
  • 김성윤 (한국건강관리협회 서울서부지부) ;
  • 신승용 (국군수도병원 순환기내과) ;
  • 양지현 (국군수도병원 순환기내과) ;
  • 우종신 (국군수도병원 순환기내과) ;
  • 김덕경 (성균관대학교 의과대학 삼성서울병원 심장혈관센터 순환기내과) ;
  • 차훈석 (성균관대학교 의과대학 삼성서울병원 류마티스내과) ;
  • 김성순 (국군수도병원 순환기내과)
  • Received : 2012.05.02
  • Accepted : 2013.03.04
  • Published : 2014.01.01
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Abstract

Atrioventricular conduction disturbance is a rare clinical manifestation of Behçet disease. We describe a case in which a 48-year-old man complaining of dyspnea on exertion presented with complete atrioventricular block with junctional escape rhythm caused by Behçet disease. He also had moderate aortic regurgitation and mitral regurgitation. MRI and PET scan revealed inflammatory changes involving the ventricular septum and the ascending aorta. Recovery of atrioventricular conduction and improvement of valvular regurgitation were achieved with immunotherapy. Timely diagnosis and treatment of cardiac Behçet disease can prevent unnecessary pacemaker implantation.

적기에 베체트병의 심혈관침범을 진단하여 면역억제치료를 시작함으로써 방실전도장애가 호전되어 영구형 심장박동기 삽입을 예방할 수 있었던 환자 1예를 보고하는 바이다.

Keywords

References

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