The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Sclerosing Angiomatoid Nodular Transformation of the Spleen: Spoke Wheel Pattern on Computed Tomography

Sclerosing Angiomatoid Nodular Transformation of Spleen 1예: 스포크 휠(Spoke Wheel) 모양의 조영증강

  • Park, Joo Han (Department of Hematology-Oncology, Ajou University School of Medicine) ;
  • Hwang, Sun Hyuk (Department of Hematology-Oncology, Ajou University School of Medicine) ;
  • Kim, Ki Chan (Department of Hematology-Oncology, Ajou University School of Medicine) ;
  • Kim, Si Yeon (Department of Hematology-Oncology, Ajou University School of Medicine) ;
  • Song, Ga Won (Department of Hematology-Oncology, Ajou University School of Medicine) ;
  • Han, Jae Ho (Department of Pathology, Ajou University School of Medicine) ;
  • Park, Joon Seong (Department of Hematology-Oncology, Ajou University School of Medicine)
  • 박주한 (아주대학교 의과대학 아주대학교병원 혈액종양내과) ;
  • 황선혁 (아주대학교 의과대학 아주대학교병원 혈액종양내과) ;
  • 김기찬 (아주대학교 의과대학 아주대학교병원 혈액종양내과) ;
  • 김시연 (아주대학교 의과대학 아주대학교병원 혈액종양내과) ;
  • 송가원 (아주대학교 의과대학 아주대학교병원 혈액종양내과) ;
  • 한재호 (아주대학교 의과대학 아주대학교병원 병리과) ;
  • 박준성 (아주대학교 의과대학 아주대학교병원 혈액종양내과)
  • Received : 2013.06.20
  • Accepted : 2013.10.01
  • Published : 2014.03.01
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Abstract

Sclerosing angiomatoid nodular transformation (SANT) is a rare, benign vascular neoplasm. Most patients have no clinical symptoms, and the tumors are usually discovered incidentally on abdominal computed tomography or ultrasonography. Some studies have reported the clinical features and imaging findings of SANT, but the diagnosis is based on histopathologic examination of a tissue specimen obtained at splenectomy. We report herein an incidentally discovered case of SANT and review the related literature.

SANT는 비장에 발생하는 매우 드문 양성 종양으로 대부분은 증상이 없어 우연히 발견되는 경우가 대부분이며 영상학적으로 확진이 어렵기 때문에 수술적 절제술을 시행하고 병리조직검사를 통해 진단을 내리게 된다. SANT는 현재까지 세계적으로 보고된 증례가 많지 않으며 그 특징이 명확히 보고된 바 없어 SANT 증례에 대해 보고하고 그 감별점에 대해 고찰하는 바이다.

Keywords

References

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