Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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Congenital Thoracic Ectopic Kidney associated with Diaphragmatic Hernia in a 15-month-old Boy

선천성 횡격막 탈장과 동반된 이소성 흉강내 신장 1례

  • Yang, Eu Jeen (Department of Pediatrics, Chonbuk National University Medical School) ;
  • Jeong, Yeon Jun (Department of Surgery, Chonbuk National University Medical School) ;
  • Hwang, Pyoung Han (Department of Pediatrics, Chonbuk National University Medical School) ;
  • Lee, Dae-Yeol (Department of Pediatrics, Chonbuk National University Medical School) ;
  • Kim, Min Sun (Department of Pediatrics, Chonbuk National University Medical School)
  • 양유진 (전북대학교 의학전문대학원 소아청소년과) ;
  • 정연준 (전북대학교 의학전문대학원 외과) ;
  • 황평한 (전북대학교 의학전문대학원 소아청소년과) ;
  • 이대열 (전북대학교 의학전문대학원 소아청소년과) ;
  • 김민선 (전북대학교 의학전문대학원 소아청소년과)
  • Received : 2014.04.24
  • Accepted : 2014.05.29
  • Published : 2014.10.31
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Abstract

Congenital thoracic ectopic kidney is a very rare developmental disorder and the rarest type of ectopic kidney. This condition is usually asymptomatic and detected incidentally on routine chest radiography. Most cases of thoracic ectopic kidney develop in adulthood and during the neonatal period, and congenital thoracic ectopic kidney rarely develops in children. Most patients are asymptomatic, and the treatment depends on the diagnosis. Herein, we report a rare case of ectopic thoracic kidney associated with a diaphragmatic hernia in a 15-month-old male infant, who presented with periodic severe irritability. The thoracic ectopic kidney was detected as a mass in the right base of the chest on routine chest radiography.

선천성 흉강내 신장은 이소성 신장의 가장 드문 형태로 알려져 있다. 흔히 증상이 없어 우연히 흉부 방사선 촬영을 통해 발견 되며, 주로 성인 시기와 산전 진단에서 진단 받는 경우가 많은 것으로 알려져 있다. 선천성 흉강내 신장은 다른 동반기형이 없는 무증상의 경우 수술적 치료가 필요하지 않으며, 횡격막 탈장이 동반된 경우 출생 후 수일 이내에 교정 수술이 필요 하다. 이에 저자들은 분만력, 과거력상 특이 소견이 없었던 15개월 남아로 간헐적인 심한 보챔을 주소로 내원하였고 흉부 방사선 촬영에서 종격동 종괴를 보여 시행한 초음파와 스캔에서 신장 위치의 이상을 확인하였고, MRI를 통해 횡격막 탈장을 확인한 예를 경험하였기에 보고하는 바이다.

Keywords

References

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  1. Right Diaphragmatic Eventration with an Intrathoracic Kidney: Case Report and Review of the Literature vol.2018, pp.None, 2014, https://doi.org/10.1155/2018/2631391