The Journal of Korea Assosiation for Disability and Oral Health (대한장애인치과학회지)

Korean Association for Disability and Oral Health (대한장애인치과학회)
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FIBROUS DYSPLASIA CAUSING FACIAL ASYMMETRY : A CASE REPORT

안면비대칭을 유발한 섬유성이형성증 : 증례보고

  • Park, Min-Kyoung (Department of Pediatric Dentistry, College of Dentistry, Yonsei University) ;
  • Jeong, Younwook (Department of Pediatric Dentistry, College of Dentistry, Yonsei University) ;
  • Lee, Hyo-Seol (Department of Pediatric Dentistry, College of Dentistry, Yonsei University) ;
  • Song, Je-Seon (Department of Pediatric Dentistry, College of Dentistry, Yonsei University) ;
  • Choi, Byung-Jai (Department of Pediatric Dentistry, College of Dentistry, Yonsei University) ;
  • Lee, Jae-Ho (Department of Pediatric Dentistry, College of Dentistry, Yonsei University)
  • 박민경 (연세대학교 치과대학 소아치과교실) ;
  • 정연욱 (연세대학교 치과대학 소아치과교실) ;
  • 이효설 (연세대학교 치과대학 소아치과교실) ;
  • 송제선 (연세대학교 치과대학 소아치과교실) ;
  • 최병재 (연세대학교 치과대학 소아치과교실) ;
  • 이제호 (연세대학교 치과대학 소아치과교실)
  • Received : 2014.06.14
  • Accepted : 2014.06.25
  • Published : 2014.06.30
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Abstract

Fibrous dysplasia(FD) is a benign fibro-ossifying disease in which fibrous tissue replaces normal bone and marrow. Craniofacial bones, including the maxilla and mandible, are commonly involved. A 7 year-old girl visited the clinic with a chief complaint of gingival swelling around the lower left primary molar. Mild bulging of the lower left periodontal tissue was observed. Not only the mandible, but also the maxilla, zygoma, sphenoid, and temporal bones were affected by FD. Permanent tooth germs were involved in the lesions and facial asymmetry was caused by lower left bone expansion. She was scheduled for a follow-up visit at the department of pediatric dentistry and oromaxillofacial surgery.

본 증례는 연세대학교 치과대학병원 소아치과에 하악 좌측 구치부 잇몸의 팽융을 주소로 내원하여 파노라마, 컴퓨터 단층촬영 결과 두개 악안면 부위에 이환된 섬유성이형성증으로 진단되었으며, 하악 좌측골의 팽윤과 안모 비대칭 및 좌우 안와 비대칭 소견을 보이고 있었다. 섬유성이형성증의 두개 안면부 병소는 안면기형, 두개 비대칭 뿐만 아니라 안구돌출, 시각 손상, 안면 마비, 삼차 신경통, 청각 손실, 치아 변위 및 부정교합, 맹출지연 등을 유발할 수 있다. 따라서 환아에게 증상이 발생할 수 있음을 보호자에게 설명하고, 검진 및 치료를 위해 구강악안면외과와 협진을 시행하였다.

Keywords

References

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