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Massive Hemoptysis Caused by Atypical Behcet's Disease

  • Lee, Won-Young (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Hoon, Choi Se (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kim, Hyeong Ryul (Department of Thoracic and Cardiovascular Surgery, Asan Medical Center, University of Ulsan College of Medicine)
  • Received : 2013.08.14
  • Accepted : 2013.10.15
  • Published : 2014.04.05

Abstract

Pulmonary and/or bronchial aneurysm with systemic thrombophlebitis can be seen in the case of both Behcet's disease and Hughes-Stovin syndrome. These two diseases may be indistinguishable since the clinical, radiological, and histopathological findings are similar in both cases. In particular, from the perspective of pulmonary involvement, hemoptysis is the leading cause of death in both conditions and is followed by aneurysmal rupture. Here, we report a case in which surgical resection was performed for a patient presenting recurrent hemoptysis as an atypical presentation of Behcet's disease.

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References

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Cited by

  1. Hughes-Stovin syndrome with pulmonary aneurysms and renal dysfunction mimicking polyarteritis nodosa vol.2, pp.1, 2018, https://doi.org/10.1080/24725625.2017.1379168
  2. Hughes-Stovin Syndrome as an Outcome of Behçet Disease or as a Different Entity vol.51, pp.1, 2014, https://doi.org/10.5090/kjtcs.2018.51.1.64
  3. Localized Bronchial Hyperemia in Cases of Iatrogenic Hemoptysis: Clinical Presentations and Pathophysiological Mechanisms vol.99, pp.5, 2014, https://doi.org/10.1159/000499053