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Hypereosinophilic Syndrome Presenting as Intussusception in Adults

성인에서 장중첩증으로 발현된 과호산구 증후군 1예

  • Chon, Nuri (Department of Internal Medicine, Hallym Hospital) ;
  • Kim, WooJung (Department of Internal Medicine, Hallym Hospital) ;
  • Park, Sang Young (Department of Internal Medicine, Hallym Hospital) ;
  • Kim, Kwang Hyun (Department of Internal Medicine, Hallym Hospital)
  • Received : 2014.02.19
  • Accepted : 2014.05.29
  • Published : 2014.11.01

Abstract

Hypereosinophilic syndrome (HES) is characterized by persistent eosinophilia associated with damage to multiple organs. Although the diagnostic criteria for HES include sustained hypereosinophilia for at least 6 months, early initiation of therapy may be recommended in patients exhibiting HES symptoms. Eosinophilic enteritis has been reported as a cause of intussusception in several cases. However, HES as a cause of intussusception has not yet been reported. In the present report, we describe a case of HES that manifested as jejunojejunal intussusception. Although long-standing hypereosinophilia was not confirmed, the patient required eosinophil-lowering therapy for an intestinal obstruction. The patient was treated with systemic corticosteroids, after which the symptoms and multiple organ involvement, including intussusception, improved dramatically, as noted on the radiological investigation. Moreover, surgery was not necessary.

Keywords

References

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