대한장애인치과학회지 (The Journal of Korea Assosiation for Disability and Oral Health)

  • 제10권2호
  • /
  • Pages.101-105
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  • 2014
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  • 1738-8813(pISSN)
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  • 2287-7142(eISSN)
대한장애인치과학회 (Korean Association for Disability and Oral Health)
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Oral findings and dental management of a patient with Moebius syndrome: a case report

  • Lee, Eunkyoung (Department of Pediatric Dentistry, School of Dentistry, Kyungpook National University) ;
  • Kim, Youngjin (Department of Pediatric Dentistry, School of Dentistry, Kyungpook National University) ;
  • Kim, Hyunjung (Department of Pediatric Dentistry, School of Dentistry, Kyungpook National University) ;
  • Nam, Soonhyeun (Department of Pediatric Dentistry, School of Dentistry, Kyungpook National University)
  • 투고 : 2014.11.28
  • 심사 : 2014.12.24
  • 발행 : 2014.12.31
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초록

Moebius syndrome is a rare, congenital neurological disease involving facial paralysis and limitation of eye movements. It results from maldevelopment of the sixth and seventh cranial nerves. Dental features of this syndrome include micrognathia, microstomia, tongue deformity, cleft palate, hypoplasia of the teeth, and congenital missing teeth. A 7-year-old female with Moebius syndrome was referred from a local dental clinic for caries treatment. She presented with facial paralysis and microstomia. Oral findings included multiple caries with enamel hypoplasia, congenital missing teeth, and tongue deformity. Dental treatments including restorative and preventive procedures were performed. Oral findings and management aspects of Moebius syndrome for this case are discussed. Early evaluation and multidisciplinary care are needed for children with Moebius syndrome.

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참고문헌

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