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Split Cord Malformation Combined with Tethered Cord Syndrome in an Adult

  • Kim, Young Deok (Department of Neurosurgery, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea) ;
  • Sung, Ji Hoon (Department of Neurosurgery, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea) ;
  • Hong, Jae Taek (Department of Neurosurgery, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea) ;
  • Lee, Sang Won (Department of Neurosurgery, St. Vincent's Hospital, College of Medicine, The Catholic University of Korea)
  • 투고 : 2013.01.04
  • 심사 : 2013.10.18
  • 발행 : 2013.10.28

초록

Split cord malformations (SCMs) usually present in childhood, and are rarely reported in adults. And also, a cervicothoracic SCM associated with tethered cord syndrome has very rarely been reported in the literature. We report a case of SCM associated with tethered cord and spina bifida in an adult. This report describes the case of a 34-year-old woman who presented for evaluation of neck pain, back pain, and intermittent paraparesis of several months duration. The MRI and CT showed a SCM at the cervicothoracic level and a fibrous septum at the thoracic level. She underwent surgery for the SCM and tethered cord syndrome, and was followed for 7 years. Patient presented complete recovery in the follow-up. The authors discuss this unusual lesion and describe the anatomical relationship of the level of cord duplication and fibrous septum.

키워드

참고문헌

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피인용 문헌

  1. Cutting filum terminale is very important in split cord malformation cases to achieve total release vol.31, pp.3, 2013, https://doi.org/10.1007/s00381-014-2586-1
  2. Type I split cord malformation and tethered cord syndrome in an adult patient: A case report and literature review vol.10, pp.None, 2013, https://doi.org/10.25259/sni-66-2019
  3. Tethered cord syndrome and transitional vertebrae vol.42, pp.2, 2020, https://doi.org/10.1007/s00276-019-02341-5