Korean Journal of Radiology

The Korean Society of Radiology (대한영상의학회)
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Magnetic Resonance Evaluation of M$\ddot{u}$llerian Remnants in Mayer-Rokitansky-K$\ddot{u}$ster-Hauser Syndrome

  • Yoo, Roh-Eul (Department of Radiology, Seoul National University Hospital) ;
  • Cho, Jeong Yeon (Department of Radiology, Seoul National University Hospital) ;
  • Kim, Sang Youn (Department of Radiology, Seoul National University Hospital) ;
  • Kim, Seung Hyup (Department of Radiology, Seoul National University Hospital)
  • Published : 2013.04.01
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Abstract

Objective: To analyze magnetic resonance imaging (MRI) findings of M$\ddot{u}$llerian remnants in young females clinically suspected of Mayer-Rokitansky-K$\ddot{u}$ster-Hauser (MRKH) syndrome in a primary amenorrhea workup. Materials and Methods: Fifteen young females underwent multiplanar T2- and transverse T1-weighted MRI at either a 1.5T or 3.0T MR imager. Two gynecologic radiologists reached consensus decisions for the evaluation of M$\ddot{u}$llerian remnants, vagina, ovaries, and associated findings. Results: All cases had bilateral uterine buds in the pelvic cavity, with unilateral cavitation in two cases. The buds had an average long-axis diameter of 2.64 ${\pm}$ 0.65 cm. In all cases, bilateral buds were connected with fibrous band-like structures. In 13 cases, the band-like structures converged at the midline or a paramedian triangular soft tissue lying above the bladder dome. The lower one-third of the vagina was identified in 14 cases. Fourteen cases showed bilateral normal ovaries near the uterine buds. One unilateral pelvic kidney, one unilateral renal agenesis, one mild scoliosis, and three lumbar sacralization cases were found as associated findings. Conclusion: Typical M$\ddot{u}$llerian remnants in MRKH syndrome consist of bilateral uterine buds connected by the fibrous bandlike structures, which converge at the midline triangular soft tissue lying above the bladder dome.

Keywords

References

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