Abstract
Pulmonary artery stenosis that causes pulmonary hypertension is usually observed in congenital anomalies and is seldom observed in adults. A 47-year-old female patient came to the hospital for aggravated dyspnea and peripheral edema. Severe pulmonary hypertension was found on an echocardiography examination, along with dilation of the main pulmonary artery and alias flow at the bifurcation sites of both pulmonary arteries. Under coronary angio-computed tomography, 70% high grade stenosis was observed on both sides of the proximal pulmonary arteries without showing atherosclerotic plaque or a thrombus. The patient's symptoms improved after performing pulmonary artery angiography and angioplasty. Thus, we report our experience of a patient with Behçet's disease and severe pulmonary hypertension caused by pulmonary artery stenosis, which was treated with percutaneous pulmonary angioplasty.
선천적 원인이 아닌 성인에서의 폐동맥협착에 의한 폐고혈압은 매우 드물게 발견된다. 베흐체트병을 앓고 있는 환자에서 호흡곤란 및 안면부종을 주소로 내원, 실시한 심초음파 검사와 심혈관 컴퓨터 단층촬영에서 폐동맥 근위부 협착이 동반되어 있음을 확인하였다. 혈관 풍선 성형술로 임상적인 증상완화 및 폐혈류량 증가, 폐동맥압의 감소를 유도할 수 있었다. 1년간의 경과관찰에서 경미한 폐동맥 직경의 감소 및 폐동맥압의 상승이 관찰되었으나 뚜렷한 증상의 악화는 없었다.