The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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Spontaneous Renal Artery Dissection in a Patient with Protein C and S Deficiency

단백질 C와 S 결핍증 환자에서 발생한 자발성 신동맥 박리 1예

  • Lim, Ye Jee (Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Lee, Rae Seok (Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Yu, Hyun Ah (Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Chang, Kyung Yoon (Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Seo, Jae Hyun (Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Lee, Kwan Hyun (Department of Internal Medicine, Cheongju St. Mary Hospital) ;
  • Hwang, Dae Yeon (Department of Internal Medicine, Cheongju St. Mary Hospital)
  • 임예지 (가톨릭대학교 의과대학 내과학교실) ;
  • 이래석 (가톨릭대학교 의과대학 내과학교실) ;
  • 유현아 (가톨릭대학교 의과대학 내과학교실) ;
  • 장경윤 (가톨릭대학교 의과대학 내과학교실) ;
  • 서재현 (가톨릭대학교 의과대학 내과학교실) ;
  • 이관현 (청주성모병원 내과) ;
  • 황대연 (청주성모병원 내과)
  • Published : 2013.01.01
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Abstract

Spontaneous renal artery dissection without aortic dissection in normotensive patients is rarely reported. Spontaneous renal artery dissection is also an uncommon cause of renal infarction that occurs, though rarely, in patients with hypercoagulable states such as protein C and S deficiency. We report here a case of spontaneous renal artery dissection and renal infarction associated with protein C and S deficiency.

일반적으로 임상에서 신동맥 박리는 대동맥 박리와 연관되어 발생하지만, 외상이나 기저질환이 없이 저절로 발생하는 자발성 신동맥 박리의 경우 알려진 다른 원인이 없거나 반복적인 동정맥 혈전증의 병력이 있을 경우 단백질 C, 단백질 S 등 혈액학적 이상을 확인할 필요가 있겠다. 이에 저자들은 자발성 신동맥 박리와 단백질 C와 S 결핍증이 동반되어 있는 환자를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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