Childhood Kidney Diseases

Korean Society of Pediatric Nephrology (대한소아신장학회)
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A Female Infant with Segmental Multicystic Dysplastic Kidney

분절형 다낭성 이형성신 영아 보고 1례

  • Lee, Jun Ho (Departments of Pediatrics, CHA Bundang Medical Center, CHA University) ;
  • Kim, Moon Kyu (Departments of Pediatrics, CHA Bundang Medical Center, CHA University)
  • 이준호 (차의과학대학교 소아과학교실) ;
  • 김문규 (차의과학대학교 소아과학교실)
  • Received : 2012.10.27
  • Accepted : 2012.12.04
  • Published : 2013.04.30
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Abstract

There have only been 35 pediatric cases and one adult case reported on segmental multicystic dysplastic kidney (MCDK) from our search in PubMed, including 19 cases detected antenatally. There is little documentation of segmental MCDK, particularly concerning its natural history. Segmental MCDK can be presented atypically, making diagnosis more difficult. We report an another case with segmental MCDK. Multicystic abdominal mass detected on antenatal sonogram in this infant was diagnosed as segmental MCDK by renal ultrasonography and computed tomography. If a definitive diagnosis of segmental MCDK can be made on imaging, surgery is not required for a diagnostic biopsy.

분절형 다낭성 이형성신은 PubMed의 자료 수집에 따르면 산전에 발견된 19명을 포함해 35명의 소아 환자와 1명의 성인 환자의 증례가 보고 되었다. 분절형 다낭성 이형성신에 대한 기록은 부족하며 비전형적으로 나타날 수 있어 진단이 어렵다. 본 연구에서는 분절형 다낭성 이형성신의 37번째 케이스를 보고하는 바다. 본 연구에서 환아의 산전 초음파에서 발견된 다낭성 복부 종양은 신장 초음파와 컴퓨터 단층촬영에 의해 분절형 다낭성 이형성신으로 진단되었다. 영상 검사를 통해 분절형 다낭성 이형성신의 최종 진단이 내려진다면 진단적 생검을 위한 수술은 불필요할 것이다.

Keywords

References

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