Korean Journal of Radiology

The Korean Society of Radiology (대한영상의학회)
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An Immunoglobulin G4-Related Sclerosing Disease of the Small Bowel: CT and Small Bowel Series Findings

  • Ko, Younghwan (Department of Radiology, Hallym University Dongtan Sacred Heart Hospital) ;
  • Woo, Ji Young (Department of Radiology, Hallym University Kangnam Sacred Heart Hospital) ;
  • Kim, Jeong Won (Department of Pathology, Hallym University Kangnam Sacred Heart Hospital) ;
  • Hong, Hye Sook (Department of Radiology, Hallym University Kangnam Sacred Heart Hospital) ;
  • Yang, Ik (Department of Radiology, Hallym University Kangnam Sacred Heart Hospital) ;
  • Lee, Yul (Department of Radiology, Hallym University Kangnam Sacred Heart Hospital) ;
  • Hwang, Daehyun (Department of Radiology, Hallym University Dongtan Sacred Heart Hospital) ;
  • Min, Seon Jeong (Department of Radiology, Hallym University Dongtan Sacred Heart Hospital)
  • Received : 2013.03.19
  • Accepted : 2013.06.11
  • Published : 2013.09.01
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Abstract

Immunoglobulin G4 (IgG4)-related sclerosing disease is rare and is known to involve various organs. We present a case of histologically proven IgG4-related sclerosing disease of the small bowel with imaging findings on computed tomography (CT) and small bowel series. CT showed irregular wall thickening, loss of mural stratification and aneurysmal dilatation of the distal ileum. Small bowel series showed aneurysmal dilatations, interloop adhesion with traction and abrupt angulation.

Keywords

References

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