The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Henoch-Sch$\ddot{o}$nlein Purpura Presenting with Cholestatic Hepatitis

담즙정체간염을 동반한 헤노흐-쇤라인자색반 1예

  • Shin, Bong Chul (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Heo, Nae-Yun (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Kang, Mi-Seon (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Lee, Ju Won (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Park, Seunghyun (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Jin, Kyubok (Department of Internal Medicine, Haeundae Paik Hospital, Inje University College of Medicine) ;
  • Kang, Jun (Department of Pathology, Haeundae Paik Hospital, Inje University College of Medicine)
  • 신봉철 (인제대학교 의과대학 해운대백병원 내과) ;
  • 허내윤 (인제대학교 의과대학 해운대백병원 내과) ;
  • 강미선 (인제대학교 의과대학 해운대백병원 내과) ;
  • 이주원 (인제대학교 의과대학 해운대백병원 내과) ;
  • 박승현 (인제대학교 의과대학 해운대백병원 내과) ;
  • 진규복 (인제대학교 의과대학 해운대백병원 내과) ;
  • 강준 (인제대학교 의과대학 해운대백병원 병리과)
  • Received : 2012.08.02
  • Accepted : 2012.10.11
  • Published : 2013.06.01
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Abstract

Hepatobiliary involvement is a rare manifestation of Henoch-Sch$\ddot{o}$nlein purpura (HSP). HSP cases related to hepatitis A, B or C virus have been reported but little is known about HSP cases complicated by cholestatic hepatitis without underlying hepatobiliary disease. Here, we report a case of Henoch-Sch$\ddot{o}$nlein purpura presenting with cholestatic hepatitis. The patient presented with upper abdominal pain and cholestasis that developed characteristic purpura. The patient was treated conservatively by therapeutic fasting and nutritional support, and liver function recovered 7 weeks after admission.

저자들은 47세 남자에게서 담즙정체간염을 동반한 헤노흐-쇤라인자반병 1예를 경험하였다. HAV, HBV, HCV와 관련된 HSP가 간기능 이상을 동반하는 경우가 보고된 바 있으나 이러한 기저 간질환 없이 HSP가 간기능 이상을 동반하는 경우는 매우 드물다. HSP 환자에게서 간기능 이상 소견 시 본 증례와 같이 다른 간담도계 질환이 없음에도 특발성으로 담즙정체간염이 나타날 수 있음을 염두에 두어야 할 것이다.

Keywords

References

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