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Primary Neuroendocrine Carcinoma of the Esophagus

식도에 발생한 원발성 신경내분비암 1예

  • Park, Ja Be (Department of Internal Medicine, Sahmyook Medical Center) ;
  • Chung, Jae Il (Department of Internal Medicine, Sahmyook Medical Center) ;
  • Yoon, Jin Won (Department of Internal Medicine, Sahmyook Medical Center) ;
  • Seol, Myung Do (Department of Internal Medicine, Sahmyook Medical Center) ;
  • Won, Dong Jun (Department of Internal Medicine, Sahmyook Medical Center) ;
  • Cho, Hye Jae (Department of Pathology, Sahmyook Medical Center) ;
  • Lee, Je Jin (Department of Thoracic Sugery, Sahmyook Medical Center)
  • Received : 2012.06.13
  • Accepted : 2012.09.19
  • Published : 2013.06.01

Abstract

Esophageal neuroendocrine carcinomas are very rare and have a poor prognosis. In addition, the optimum treatment has not been established due to the rarity of the condition. An accurate differential diagnosis is important because treatments and clinical courses differ from those of esophageal squamous cell carcinomas. We report a case of a 61-year-old female who underwent endoscopy for dysphagia and was diagnosed with a neuroendocrine carcinoma of the esophagus, which was successfully resected by esophagectomy.

식도 신경내분비암종은 매우 드물고 예후가 나쁘다. 또한 질환의 희귀성으로 인해 치료체계가 확립되지 않은 질환이다. 식도 악성종양의 대부분을 차지하는 상피세포암과는 치료방법 및 임상경과가 달라 정확한 감별 진단이 필요하다. 이에 저자들은 연하곤란을 이유로 시행한 상부위장관 내시경에서 식도의 종양이 발견되어 내시경적 조직 생검 시행 후 신경내분비암종으로 진단되어 식도 절제술로 치료한 61세 여자 환자 증례를 보고하는 바이다.

Keywords

References

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