The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Asymptomatic Severe Pulmonary Valve Stenosis with Patent Foramen Ovale and Patent Ductus Arteriosus in an Adult

성인에서 폐동맥판협착과 난원공개존증을 동반한 동맥관개존증 1예

  • Kim, Seon A (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Her, Sung-Ho (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Park, Mahn Won (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Na, Soo Jin (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Hyung Duk (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Ji Eun (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine) ;
  • Kim, Woo Hyeon (Division of Cardiology, Department of Internal Medicine, The Catholic University of Korea College of Medicine)
  • 김선아 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 허성호 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 박만원 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 나수진 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김형덕 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김지은 (가톨릭대학교 의과대학 내과학교실 심장내과) ;
  • 김우현 (가톨릭대학교 의과대학 내과학교실 심장내과)
  • Received : 2012.08.31
  • Accepted : 2012.11.02
  • Published : 2013.10.01
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Abstract

Pulmonary valve stenosis (PS) is the 3rd most common form of adult congenital heart disease. The patient was a 56-year-old woman, with known congenital heart disease but who was not receiving any treatment as she was not functionally limited. A two-dimensional echocardiogram showed severe right ventricular hypertrophy, pulmonary valve thickening and systolic doming. A color Doppler revealed a retrograde flow from the aorta to the left pulmonary artery. She had severe heart failure on the right hand side from a PS but did not display any symptoms. We hypothesized that she had a retrograde flow to the pulmonary circulation through a patent ductus arteriosus (PDA), through which oxygenated blood could be supplied to the systemic circulation and, hence, no hypoxia. We attempted a balloon valvuloplasty for the PS followed by a device closure for the PDA. Here we report on this adult female with severe PS but lacking any symptoms, due to the presence of a PDA.

저자들은 중증 폐동맥판협착과 난원공개존증이 있음에도 동맥관개존증이 동반되어 무증상으로 나타난 성인에서의 증례를 경험하였기에 이를 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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