Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Meningeal Supratentorial Hemangioblastoma in a Patient with Von Hippel-Lindau Disease Mimicking Angioblastic Menigioma

  • Kim, Hoon (Department of Neurosurgery, The Catholic University of Korea College of Medicine, Bucheon St. Mary's Hospital) ;
  • Park, Ik-Seong (Department of Neurosurgery, The Catholic University of Korea College of Medicine, Bucheon St. Mary's Hospital) ;
  • Jo, Kwang-Wook (Department of Neurosurgery, The Catholic University of Korea College of Medicine, Bucheon St. Mary's Hospital)
  • Received : 2012.10.25
  • Accepted : 2013.11.07
  • Published : 2013.11.28
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Abstract

Hemangioblastomas are sporadic tumors found in the cerebellum or spinal cord. Supratentorial hemangioblastomas are rare, and those with meningeal involvement are extremely rare and have been reported in only approximately 130 patients. Here, we report the case of a 51-year-old female patient with supratentorial meningeal hemangioblastoma detected 5 years after surgical resection of an infratentorial hemangioblastoma associated with von Hippel-Lindau disease. Patients with von Hippel-Lindau syndrome are at risk for developing multiple hemangioblastomas, with new tumor formation and growth and possible meningeal infiltration. Regular lifelong follow-up in at-risk patients is recommended and should include the differential diagnosis of dural-based tumors such as angioblastic meningioma and metastatic renal cell carcinoma.

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