Clinical and Experimental Pediatrics

The Korean Pediatric Society (대한소아청소년과학회)
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Moyamoya syndrome occurred in a girl with an inactive systemic lupus erythematosus

  • Lee, Yun-Jin (Department of Pediatrics, Pusan National University Children's Hospital, Pusan National University School of Medicine) ;
  • Yeon, Gyu Min (Department of Pediatrics, Pusan National University Children's Hospital, Pusan National University School of Medicine) ;
  • Nam, Sang Ook (Department of Pediatrics, Pusan National University Children's Hospital, Pusan National University School of Medicine) ;
  • Kim, Su Yung (Department of Pediatrics, Pusan National University Children's Hospital, Pusan National University School of Medicine)
  • Received : 2012.10.06
  • Accepted : 2013.05.09
  • Published : 2013.12.31
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Abstract

We report the case of a 17-year-old Korean girl with systemic lupus erythematosus (SLE) who presented with sudden weakness of the right-sided extremities and dysarthria. Oral prednisolone was being taken to control SLE. Results of clinical and laboratory examinations did not show any evidence of antiphospholipid syndrome or thromboembolic disease nor SLE activity. Cerebral angiography showed stenosis of the left internal carotid artery and right anterior cerebral artery with accompanying collateral circulation (moyamoya vessels). After the patient underwent bypass surgery on the left side, she recovered from the neurological problems and did not experience any additional ischemic attack during the 14-month follow-up period. This case represents an unusual association between moyamoya syndrome and inactive SLE (inactive for a relatively long interval of 2 years) in a young girl.

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References

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