Tuberculosis and Respiratory Diseases

The Korean Academy of Tuberculosis and Respiratory Diseases (대한결핵및호흡기학회)
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A Case of Pulmonary Artery Intimal Sarcoma Masquerading as Pulmonary Embolism

폐색전증으로 오인된 폐동맥내막육종 1예

  • Kim, Jin-Suk (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Park, Hye-Kyeong (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Lee, Hye-Ran (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Kang, Seung-Dae (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Bae, Sang-Chul (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Kim, Su-Young (Department of Radiology, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Chang, Sun-Hee (Department of Pathology, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Chang, Woo-Ik (Department of Cardiosurgery, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Kang, Seung-Hee (Department of Radiation Oncology, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Lee, Sung-Soon (Department of Internal Medicine, Ilsan Paik Hospital, Inje University College of Medicine)
  • 김진숙 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 박혜경 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 이혜란 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 강승대 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 배상철 (인제대학교 의과대학 일산백병원 내과학교실) ;
  • 김수영 (인제대학교 의과대학 일산백병원 영상의학교실) ;
  • 장선희 (인제대학교 의과대학 일산백병원 병리학교실) ;
  • 장우익 (인제대학교 의과대학 일산백병원 흉부외과학교실) ;
  • 강승희 (인제대학교 의과대학 일산백병원 치료방사선과학교실) ;
  • 이성순 (인제대학교 의과대학 일산백병원 내과학교실)
  • Received : 2011.12.31
  • Accepted : 2012.02.06
  • Published : 2012.02.29
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Abstract

Pulmonary artery intimal sarcoma is a rare tumor with no characteristic symptoms. It is frequently misdiagnosed as pulmonary embolism. We report a case of pulmonary artery intimal sarcoma in a 48-year-old man with dyspnea, cough and blood-tinged sputum. He was initially suspected and treated as a pulmonary embolism. Computed tomography of the chest showed filling defects occupying the entire luminal diameter of the right and left pulmonary artery as well as extraluminal extension of the intraluminal mass. Surgical resection of the tumor confirmed pulmonary artery intimal sarcoma. After surgery, he received 8 cycles of combined chemotherapy consisting of doxorubicin and ifosfamide. After 8 cycles, Computed tomography of the chest showed interval regression of the residual tumor. Radiotherapy was done as total 6,000 cGy for 5 weeks, following the 8th chemotherapy. The patient's condition was successfully stabilized with chemotherapy and radiotherapy.

Keywords

References

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