Maxillofacial Plastic and Reconstructive Surgery

  • 제34권5호
  • /
  • Pages.357-362
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  • 2012
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  • 2288-8101(pISSN)
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  • 2288-8586(eISSN)
대한악안면성형재건외과학회 (Korean Association of Maxillofacial Plastic and Reconstructive Surgeons)
권호 표지

체루비즘: 2예 보고

Cherubism: Review of 2 Cases

  • 곽주희 (이화여자대학교 의학전문대학원 목동병원 구강악안면외과) ;
  • 김지연 (이화여자대학교 의학전문대학원 목동병원 구강악안면외과) ;
  • 김명래 (이화여자대학교 의학전문대학원 목동병원 구강악안면외과) ;
  • 김선종 (이화여자대학교 의학전문대학원 목동병원 구강악안면외과)
  • Kwak, Juhee (Department of Oral and Maxillofacial Surgery, Ewha Womans University Mokdong Hospital, Ewha Womans University School of Medicine) ;
  • Kim, Ji-Youn (Department of Oral and Maxillofacial Surgery, Ewha Womans University Mokdong Hospital, Ewha Womans University School of Medicine) ;
  • Kim, Myung-Rae (Department of Oral and Maxillofacial Surgery, Ewha Womans University Mokdong Hospital, Ewha Womans University School of Medicine) ;
  • Kim, Sun-Jong (Department of Oral and Maxillofacial Surgery, Ewha Womans University Mokdong Hospital, Ewha Womans University School of Medicine)
  • 투고 : 2012.05.17
  • 심사 : 2012.08.27
  • 발행 : 2012.09.30
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초록

Cherubism is a rare familial disease of childhood, characterized by proliferative lesion, which is within the maxilla and mandible. In a typical case, painless symmetric expansile lesions develop in the jaws. It shows substitution of the bone by proliferating fibrous tissue exhibiting mature fibroblasts and a number of multinucleated giant cells within an intercellular matrix. Usually, the disease manifests in early childhood, and becomes more marked until puberty, at which time the bony lesions begin to regress. As such, conservative approaches to management are advisable. However, excision of tissue through enucleation or curettage appears to be necessary in more aggressive cases, to reduce the maxillofacial deformity after puberty and to ensure a successful outcome without the risk of progression, requiring additional resection. This report describes 2 cases of manifestation of cherubism of oral and maxillofacial region. We present diagnosis, radiological - histopathologic features, and treatment of cherubism.

키워드

참고문헌

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