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BURKITT'S LYMPHOMA OF THE MANDIBLE IN A CHILD

어린이의 하악골에서 발생한 Burkitt 림프종

  • Lee, Soo-Eon (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University) ;
  • Sohn, Mi-Yeon (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University) ;
  • Choi, Sung-Chul (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University) ;
  • Kim, Kwang-Chul (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University) ;
  • Park, Jae-Hong (Department of Pediatric Dentistry, School of Dentistry, Kyung Hee University)
  • 이수언 (경희대학교 치의학전문대학원 소아치과학교실) ;
  • 손미연 (경희대학교 치의학전문대학원 소아치과학교실) ;
  • 최성철 (경희대학교 치의학전문대학원 소아치과학교실) ;
  • 김광철 (경희대학교 치의학전문대학원 소아치과학교실) ;
  • 박재홍 (경희대학교 치의학전문대학원 소아치과학교실)
  • Received : 2011.10.10
  • Accepted : 2012.01.10
  • Published : 2012.02.29

Abstract

Burkitt's lymphoma is a malignant tumor originated from B lymphocyte and a type of non-hodgkin lymphoma. It is clinically classified by endemic, sporadic and immune deficient forms. In the past, it had poor prognosis but in recent years survival rate is 50~80% treated by intensive chemotherapeutic regimens. Mostly it is a lesion of the jaws. Clinical symptoms are severe tooth mobility, displacement, gingival redness and swelling. This case is about a patient with aggressively progressing Burkitt's lymphoma of the jaws. Initial diagnosis was done in dental hospital and it has shown satisfactory outcome by prompt and appropriate treatment.

Burkitt 림프종은 B림프구 기원의 악성종양으로 비호지킨 림프종(non-Hodgkin's lymphoma)의 한 종류이다. Burkitt 림프종은 임상적으로 아프리카에서 나타나는 지역형(endemic), 세계 각지에서 발생하는 산발형(sporadic), 면역결핍상태와 관련되어 나타나는 형태로 나눌 수 있다. 과거에는 그 예후가 매우 불량했으나, 최근에는 집중적인 화학요법으로 인한 치료 성공률이 50-80%에 달한다. 많은 경우 악골을 포함하고 있으며 임상증상으로는 심하게 흔들리는 치아, 치아의 변위 그리고 치은의 발적 및 부종 등이 있다. 본 증례는 진행속도가 상당히 빠른 Burkitt 림프종에 이환된 환아에 대한 내용이다. 악골에 생긴 병소로 내원하였으며, 치과에서 처음 진단하였고 신속하고 적절한 치료를 통해 양호한 결과를 얻었다.

Keywords

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  1. Early Diagnosis of Burkitt Lymphoma on the Mandible: A Case Report vol.43, pp.4, 2016, https://doi.org/10.5933/JKAPD.2016.43.4.452