DOI QR코드

DOI QR Code

Ewing's Sarcoma of the Lesser Sac Masquerading as a Pancreatic Tumor

  • Rao, Lakshmi (Department of Pathology, Kasturba Medical College) ;
  • Monappa, Vidya (Department of Pathology, Kasturba Medical College) ;
  • Rodrigues, Gabriel (Department of Surgery, Kasturba Medical College and Kasturba Hospital) ;
  • Suresh, B.P. (Department of Surgery, Kasturba Medical College and Kasturba Hospital)
  • Published : 2012.03.01

Abstract

Extraosseous Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is an uncommon, aggressive, and malignant tumor with a poor patient outcome. Its occurrence in the lesser sac is a rare event and to the best of our knowledge, has not been previously described. The present case was clinically and radiologically misdiagnosed as a pancreatic tumor/gastrointestinal stromal tumor. Histopathology revealed a tumor with "small round cells" that were positive for CD99, confirming the diagnosis of ES/PNET. This report highlights the importance of considering Ewing's sarcoma in the differential diagnosis of intraabdominal, extraintestinal masses.

Keywords

References

  1. Kim SW, Shin H. Primary intradural extraosseous Ewing's sarcoma. J Korean Neurosurg Soc 2009;45:179-181. https://doi.org/10.3340/jkns.2009.45.3.179
  2. Wick MR, Nappi O. Ectopic neural and neuroendocrine neoplasms. Semin Diagn Pathol 2003;20:305-323. https://doi.org/10.1053/j.semdp.2003.08.006
  3. Colovic RB, Grubor NM, Micev MT, Matic SV, Atkinson HD, Latincic SM. Perigastric extraskeletal Ewing's sarcoma: a case report. World J Gastroenterol 2009;15:245-247. https://doi.org/10.3748/wjg.15.245
  4. Zagar TM, Triche TJ, Kinsella TJ. Extraosseous Ewing's sarcoma: 25 years later. J Clin Oncol 2008;26:4230-4232. https://doi.org/10.1200/JCO.2008.16.5308
  5. Montesco MC, Alaggio R, Ninfo V. Pediatric-type sarcomas in adult patients. Semin Diagn Pathol 2003;20:324-337. https://doi.org/10.1053/j.semdp.2003.08.004
  6. Gerald WL. A practical approach to the differential diagnosis of small round cell tumors of infancy using recent scientific and technical advances. Int J Surg Pathol 2000;8:87-97. https://doi.org/10.1177/106689690000800203
  7. Savastano S, d'Amore ES, Zuccarotto D, Banzato O, Beghetto M, Famengo B. Pancreatoblastoma in an adult patient: a case report. JOP 2009;10:192-195.

Cited by

  1. Extra-osseous Ewing sarcoma of the pancreas: case report with radiologic, pathologic, and molecular correlation, and brief review of the literature vol.473, pp.3, 2012, https://doi.org/10.1007/s00428-018-2344-y
  2. Intraabdominal lesser sac metastasis from Ewing’s sarcoma: An exceptional localization vol.9, pp.None, 2012, https://doi.org/10.1177/2050313x211022426