Korean Journal of Radiology

The Korean Society of Radiology (대한영상의학회)
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Intracranial Extramedullary Hematopoiesis in Beta-Thalassemia

  • Karki, Bivek (Department of Medical Imaging, Nan fang Hospital, Southern Medical University) ;
  • Kai, Xu Yi (Department of Medical Imaging, Nan fang Hospital, Southern Medical University) ;
  • Tamrakar, Karuna (Department of Neurosurgery, Zhujiang Hospital, Southern Medical University) ;
  • Kui, Wu Yuan (Department of Medical Imaging, Nan fang Hospital, Southern Medical University)
  • Published : 2012.04.01
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Abstract

Extramedullary hematopoiesis (EMH) represents tumor-like proliferation of hemopoietic tissue which complicates chronic hemoglobinopathy. Intracranial EMH is an extremely rare occurrence. Magnetic resonance imaging (MRI) offers a precise diagnosis. It is essential to distinguish EMH from other extradural central nervous system tumors, because treatment and prognosis are totally different. Herein, we report the imaging findings of beta-thalassemia in a 13-year-old boy complaining of weakness of left side of the body and gait disturbance; CT and MRI revealed an extradural mass in the right temporo-parietal region.

Keywords

References

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