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A CASE OF DELAYED ERUPTION IN A CHILD WITH MONOSTOTIC FIBROUS DYSPLASIA

단골성 섬유성이형성증 환아에서 나타난 맹출지연

  • Min, Soo-Young (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Lee, Jae-Ho (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Kim, Seong-Oh (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Choi, Byung-Jae (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Choi, Hyung-Jun (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Kim, Seung-Hye (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University) ;
  • Song, Je-Seon (Department of Pediatric Dentistry, Department of Pediatric Dentistry and Oral Science Research Center, College of Dentistry, Yonsei University)
  • 민수영 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 이제호 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 김성오 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 최병재 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 최형준 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 김승혜 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소) ;
  • 송제선 (연세대학교 치과대학 소아치과학교실 및 구강과학연구소)
  • Received : 2011.03.16
  • Accepted : 2011.06.20
  • Published : 2011.08.31

Abstract

Fibrous dysplasia is a developmental tumor-like condition that is characterized by replacement of normal bone by an excessive proliferation of cellular fibrous connective tissue intermixed with irregular bony trabeculae. Craniofacial lesions may cause facial pain, headache, cranial asymmetry, facial deformity, tooth displacement and visual or auditory impairment. In this case, a 2-year-9-month old boy who was diagnosed as the fibrous dysplasia showed delayed eruption on affected area. Teeth of left lateral dentition group have erupted completely but teeth of right lateral dentition group are erupting slowly. Eruption and maturation of affected teeth are in progress, so continuous observation is required presently. If the eruption state stops, surgical opening or forced eruption of the impacted teeth will be considered.

섬유성이형성증은 골격 계통의 국소화된 양성 발육장애로서 해면골 내에서 섬유조직이 증식되며 불규칙한 골소주가 형성되는 질환이다. 섬유성이형성증의 두개안면부 병소는 안면동통, 두통, 두개비대칭, 안면기형, 치아이동, 부정교합, 시각이상, 청각이상 등의 증상이 나타날 수 있다. 본 증례는 섬유성이형성증으로 진단된 혼합치열기 환아로서 이환 부위에서 영구치의 맹출지연이 관찰되었다. 병소에 이환되지 않은 환아의 하악 좌측 측방 치열군은 교합위까지 맹출을 완료하였으나 병소에 이환된 하악 우측 측방 치열군은 현재 치조골 내에서 느린 속도로 맹출 중이며 치근 형성이 완료되지 않아 계속 경과 관찰 중이다. 맹출이 정지되었다고 판단될 시 상부 치조골 제거를 통한 맹출유도나 교정적 정출을 고려할 수 있을 것이다.

Keywords

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  1. FIBROUS DYSPLASIA CAUSING FACIAL ASYMMETRY : A CASE REPORT vol.10, pp.1, 2014, https://doi.org/10.12655/KADH.2014.10.1.22