Journal of Korean Neurosurgical Society

The Korean Neurosurgical Society (대한신경외과학회)
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Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor in the Cerebellopontine Angle : Diagnosis and Treatment

  • Choi, Ho-Yong (Department of Neurosurgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim, Yong-Hwy (Department of Neurosurgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim, Jee-Hyun (Department of Hemato-Oncology, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Kim, In-Ah (Department of Radiation Oncology, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Choe, Ghee-Young (Department of Pathology, Seoul National University Bundang Hospital, Seoul National University College of Medicine) ;
  • Kim, Chae-Yong (Department of Neurosurgery, Seoul National University Bundang Hospital, Seoul National University College of Medicine)
  • Received : 2010.08.31
  • Accepted : 2011.05.30
  • Published : 2011.06.28
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Abstract

Ewing's sarcoma/primitive neuroectodermal tumor (ES/PNET) is an unusual malignancy with aggressive behavior. ES/PNET in the cerebellopontine angle (CPA) is extremely uncommon, and we report on a rare case here. A 31-year-old man presented with one month history of left facial palsy, hearing loss, swallowing difficulty, and hoarseness. Magnetic resonance images showed a large mass in the left CPA and a small one in the right cerebellar hemisphere. The patient underwent a surgery for the CPA mass lesion, and the pathology was compatible with ES/PNET. Radiation therapy and chemotherapy were administered. In contrast to the initial radiologic findings resembling vestibular schwannoma or meningioma, ES/PNET had several distinct clinical features. A patient with a CPA mass and presenting unusual clinical features should be suspected of having a rare malignancy.

Keywords

References

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