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Dandy-Walker Malformation Associated with Neurocutaneous Melanosis

  • Cho, In-Yong (Department of Neurosurgery, College of Medicine, Ewha Womans University) ;
  • Hwang, Sung-Kyun (Department of Neurosurgery, College of Medicine, Ewha Womans University) ;
  • Kim, Sung-Hak (Department of Neurosurgery, College of Medicine, Ewha Womans University)
  • Received : 2011.01.28
  • Accepted : 2011.11.14
  • Published : 2011.11.28

Abstract

Neurocutaneous melanosis associated with Dandy-Walker malformation is a rare dysmorphogenesis that is associated with single or multiple giant pigmented cutaneous nevi and diffuse involvement of the central nervous system. In this article, we present a 2-month-old patient with neurocutaneous melanosis associated with Dandy-Walker malformation. In addition, we reviewed the literature and discussed the pathogenesis based on the preferred hypotheses.

Keywords

References

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