Archives of Plastic Surgery

Korean Society of Plastic and Reconstructive Surgeons (대한성형외과학회)
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Malignant Peripheral Nerve Sheath Tumor of Abdomen

복부에 발생한 악성 말초신경초종양

  • So, Kyu-Sub (Department of Plastic and Reconstructive Surgery, Fatima Hospital) ;
  • Lim, Yeung-Kook (Department of Plastic and Reconstructive Surgery, Fatima Hospital) ;
  • Hong, Yong-Taek (Department of Plastic and Reconstructive Surgery, Fatima Hospital) ;
  • Kim, Hoon-Nam (Department of Plastic and Reconstructive Surgery, Fatima Hospital)
  • 소규섭 (대구파티마병원 성형외과) ;
  • 임영국 (대구파티마병원 성형외과) ;
  • 홍용택 (대구파티마병원 성형외과) ;
  • 김훈남 (대구파티마병원 성형외과)
  • Received : 2011.06.04
  • Accepted : 2011.08.03
  • Published : 2011.11.10
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Abstract

Purpose: Malignant peripheral nerve sheath tumor without neurofibromatosis type 1 is very rare neoplasm. Development in the superficial soft tissue is exremely rare. Authors experienced one rare case of primary malignant peripheral nerve sheath tumor developed on abdomen. The clinical and histologic findings were described. Methods: An 83-year-old man visited hospital with an $11{\times}6.5{\times}4.5$ cm sized ulcerated and hemorrhagic mass on abdomen. The tumor was localized in abdominal skin and started growing 3 years ago. Results: Wide excision with safety margin of 2 cm and limberg flap was done. The postoperative biopsy revealed a malignant peripheral nerve sheath tumor. There was no evidence of recurrence of tumor for 16 months. Conclusion: Malignant peripheral nerve sheath tumor is an aggressive malignant tumor. An abrupt enlargement of size, ulceration and bleeding are suggestive of malignant chnages of the tumor. We recommand early wide excision with enough safety margin as treatment of malignant peripheral nerve sheath tumor.

Keywords

References

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