Maxillofacial Plastic and Reconstructive Surgery

Korean Association of Maxillofacial Plastic and Reconstructive Surgeons (대한악안면성형재건외과학회)
권호 표지

Management of Proteus Syndrome with Craniofacial Hemihyperostosis: Case Report

악골의 편측 비대를 보이는 프로테우스 증후군의 치료: 증례보고

  • Yun, Yeong-Eun (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Seol, Ka-Young (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Oh, Min-Seok (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Choi, Jung-Goo (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Kim, Sang-Jung (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Lee, Dong-Keun (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital) ;
  • Kang, Ji-Yeon (Department of Oral and Maxillofacial Surgery, Sun Dental Hospital)
  • 윤영은 (선치과병원 구강악안면외과) ;
  • 설가영 (선치과병원 구강악안면외과) ;
  • 오민석 (선치과병원 구강악안면외과) ;
  • 최정구 (선치과병원 구강악안면외과) ;
  • 김상중 (선치과병원 구강악안면외과) ;
  • 이동근 (선치과병원 구강악안면외과) ;
  • 강지연 (선치과병원 구강악안면외과)
  • Received : 2011.09.06
  • Accepted : 2011.09.28
  • Published : 2011.11.30
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Abstract

Proteus syndrome is a congenital hamartomatous malformation that is characterized by a wide range of deformities, including craniofacial deformities. Proteus syndrome features partial gigantism and asymmetry of the limbs, plantar hyperplasia, hemangiomas, lipomas, lymphangiomas, varicosities, verrucous epidermal nevi, macrocephaly, cranial hyperostosis, and long bone overgrowth. We diagnosed Proteus syndrome in a male patient who visited our hospital with a chief complaint of limited mouth opening and report the case because we obtained a good healing outcome after treating the condition with a corrective osteotomy.

Keywords

References

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