Paratesticular Alveolar Rhabdomyosarcoma with Multiple Lymph Nodes Metastasis Successfully Treated with Chemotherapy

전이성 고환주위 폐포성 횡문근육종 1예

  • Lee, Ha-Young (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Hyun, Myung-Soo (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Lee, Kyung-Hee (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Kim, Min-Kyoung (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Koh, Sung-Ae (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Sohn, Se-Hoon (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Park, Sung-Woo (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Kim, Dong-Geun (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Kim, Myung-Jin (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Jang, Hyo-Jin (Department of Internal Medicine, College of Medicine, Yeungnam University) ;
  • Kim, Mi-Jin (Department of Pathology, College of Medicine, Yeungnam University)
  • 이하영 (영남대학교 의과대학 내과학교실) ;
  • 현명수 (영남대학교 의과대학 내과학교실) ;
  • 이경희 (영남대학교 의과대학 내과학교실) ;
  • 김민경 (영남대학교 의과대학 내과학교실) ;
  • 고성애 (영남대학교 의과대학 내과학교실) ;
  • 손세훈 (영남대학교 의과대학 내과학교실) ;
  • 박성우 (영남대학교 의과대학 내과학교실) ;
  • 김동근 (영남대학교 의과대학 내과학교실) ;
  • 김명진 (영남대학교 의과대학 내과학교실) ;
  • 장효진 (영남대학교 의과대학 내과학교실) ;
  • 김미진 (영남대학교 의과대학 병리학교실)
  • Published : 2011.06.30

Abstract

Rhabdomyosarcomas are soft tissue sarcomas; while extremely rare in adults, they are one of the most common neoplasms in children and adolescents. Histologically, they can be classified into embryonal (ERMS), alveolar (ARMS), pleomorphic, and undifferentiated types. The ARMS type is very rare, and is associated with a poor prognosis. Common primary sites of ARMS are the trunk and extremities. We report on a case of paraaortic, supraclavicular, and axillary lymph node metastasis from paratesticular ARMS treated with VAC (vincristine, dactinomycin, cyclophosphamide)/ IE(ifosfamide, etoposide) chemotherapy in a young adult. Administration of six cycles of chemotherapy with VAC/IE resulted in complete remission. The patient has maintained complete remission over the past 27 months.

Keywords