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Low-grade myxofibrosarcoma in the mandible: a case report

하악에 발생한 저등급의 점액섬유육종: 증례보고

  • Park, Ji-Hoon (Department of Oral and Maxillofacial Surgery, School of Dentistry, Kyungpook National University) ;
  • Choi, So-Young (Department of Oral and Maxillofacial Surgery, School of Dentistry, Kyungpook National University) ;
  • Kwon, Tae-Geon (Department of Oral and Maxillofacial Surgery, School of Dentistry, Kyungpook National University) ;
  • Kim, Chin-Soo (Department of Oral and Maxillofacial Surgery, School of Dentistry, Kyungpook National University)
  • 박지훈 (경북대학교 치의학전문대학원 구강악안면외과학교실) ;
  • 최소영 (경북대학교 치의학전문대학원 구강악안면외과학교실) ;
  • 권대근 (경북대학교 치의학전문대학원 구강악안면외과학교실) ;
  • 김진수 (경북대학교 치의학전문대학원 구강악안면외과학교실)
  • Received : 2010.09.26
  • Accepted : 2011.01.19
  • Published : 2011.02.28

Abstract

Myxofibrosarcoma, also known as a myxoid variant of a malignant fibrous histiocytoma (MFH), is one of the most common sarcomas in the extremities of elderly people. The lesion is characterized by a high frequency of local recurrence but is uncommon in the head and neck regions. Low-grade myxofibrosarcoma, which is commonly misinterpreted as being benign, has a tendency for histological and biological progression in local recurrences, highlighting the importance of an accurate diagnosis and wide surgical excision of the primary lesion. We report a rare case of low-grade myxofibrosarcoma of the mandible located in the left mandibular body and angle area. The tumor was first diagnosed as a myxofibroma and was resected initially. After the final biopsy the patient underwent combined chemo-radiotherapy. The progress of the patent was uneventful until the one year follow up.

Keywords

References

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