Dementia and Neurocognitive Disorders (대한치매학회지)

Korean Dementia Association (대한치매학회)
권호 표지

A Case of Nonvasculitic Autoimmune Inflammatory Meningoencephalitis Accompanied by Sj$\ddot{o}$gren's Syndrome and Elevated Antithyroid Antibodies

쉐그렌증후군과 항 갑상선 항체의 상승을 동반한 비혈관염 자가면역 염증성 뇌병증 1예

  • Lee, Seong-Joon (Department of Neurology, Ajou University School of Medicine) ;
  • Sohn, Sung-Yeon (Department of Neurology, Ajou University School of Medicine) ;
  • Lim, Tae-Sung (Department of Neurology, Ajou University School of Medicine) ;
  • Moon, So-Young (Department of Neurology, Ajou University School of Medicine)
  • 이성준 (아주대학교 의과대학 신경과학교실) ;
  • 손성연 (아주대학교 의과대학 신경과학교실) ;
  • 임태성 (아주대학교 의과대학 신경과학교실) ;
  • 문소영 (아주대학교 의과대학 신경과학교실)
  • Published : 2011.09.30
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Abstract

Background: Nonvasculitic autoimmune inflammatory meningoencephalitis (NAIM) is known to be one of the causes of potentially reversible dementia. NAIM can be accompanied by various autoimmune diseases. Methods: A 65 year-old woman had been treated with stable bipolar disorder and presented with rapid cognitive decline, visual hallucination and myoclonus. Anti-thyroid antibodies were elevated. Her symptoms were responsive to steroid therapy. Her diagnostic evaluation also revealed Sj$\ddot{o}$gren's syndrome. Although her symptoms recovered, a manic episode reappeared and was responsive to psychiatric treatment. Conclusions: Patients presenting with rapidly progressive dementia should be thoroughly evaluated for the diagnosis of NAIM, a potentially treatable form of dementia, and the possible various underlying autoimmune etiologies.

Keywords

References

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