The Korean Journal of Medicine

  • 제80권6호
  • /
  • Pages.739-744
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  • 2011
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  • 1738-9364(pISSN)
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  • 2289-0769(eISSN)
대한내과학회 (The Korean Association of Internal Medicine)
권호 표지

Henoch-Schonlein Purpura 환자에서 동반된 폐출혈 1예

A Case of Pulmonary Hemorrhage through Pulmonary Involvement of Henoch-Schonlein Purpura

  • 권용진 (연세대학교 의과대학 내과학교실) ;
  • 정수진 (연세대학교 의과대학 내과학교실) ;
  • 박민찬 (연세대학교 의과대학 내과학교실)
  • Kwon, Yong-Jin (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Chung, Soo-Jin (Department of Internal Medicine, Yonsei University College of Medicine) ;
  • Park, Min-Chan (Department of Internal Medicine, Yonsei University College of Medicine)
  • 발행 : 2011.06.01
⟨ 이전 논문 다음 논문 ⟩

초록

저자들은 피부 자반증, 복통, 혈변, 단백뇨 및 혈뇨가 발생하여 HSP로 진단된 후 급격한 폐출혈 및 이차성 폐렴이 발생하여 경정맥 항생제투여로 감염 조절 후 부신피질호르몬제 치료를 통해 폐출혈이 회복된 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Henoch-$Sch{\ddot{o}}nlein$ purpura (HSP) is an immunologically mediated systemic vasculitis of small blood vessels that primarily involves the skin, gastrointestinal tract, joints, and kidneys. HSP is a relatively common vasculitic syndrome in children, which usually resolves within several weeks, and requires no treatment. The pulmonary parenchymal involvement of HSP is a rare complication that predominantly occurs in adolescents and adults. Mortality following HSP pulmonary presentation is extremely high. Here, we report a case of HSP combined with pulmonary hemorrhage as a presentation of the vasculitic involvement of the lung. Recently, we experienced a case of a 49-year-old male patient with HSP who presented with palpable purpura, enteritis, and glomerulonephritis. Following the diagnosis of HSP, the patient developed sudden pulmonary hemorrhage due to the pulmonary involvement of vasculitis, and recovered following glucocorticoid therapy.

키워드

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