The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
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A Case of Erdheim-Chester Disease Mimicking Systemic Lymphangitic Metastasis

림프구성 전이암으로 오인된 Erdheim Chester Disease 1예

  • Sim, Yun-Su (Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute) ;
  • Park, Jin-Kyeong (Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute) ;
  • Lee, Jin-Hwa (Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute) ;
  • Song, Dong-Eun (Department of Pathology, Ewha Womans University School of Medicine, Ewha Medical Research Institute) ;
  • Chang, Jung-Hyun (Department of Internal Medicine, Ewha Womans University School of Medicine, Ewha Medical Research Institute)
  • 심윤수 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 박진경 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 이진화 (이화여자대학교 의학전문대학원 내과학교실) ;
  • 송동은 (이화여자대학교 의학전문대학원 병리학교실) ;
  • 장중현 (이화여자대학교 의학전문대학원 내과학교실)
  • Published : 2011.06.01
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Abstract

Erdheim-Chester disease (ECD) is non-Langerhans cell histiocytosis that leads to multi-organ involvement with unknown etiology. We report a 64-year-old woman with a dry cough and dyspnea. She had interlobular septal thickening and ground-glass opacity in both lungs, suggesting lymphangitic lung metastasis. However, she was diagnosed with ECD after a long bone and immunohistological evaluation.

저자들은 호흡곤란으로 내원한 환자에서 폐실질과 종격동림프절, 후복막 종괴 등을 동반한 병변을 발견하여 전신의 림프구성 전이로 오인하여 원발암을 찾는 과정에서 Erdheimchester disease를 진단하였다. 이에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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