Journal of the Korean Society of Radiology (대한영상의학회지)

The Korean Society of Radiology (대한영상의학회)
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Primary Amyloidosis Involving Mediastinal and Cervical Lymph Nodes: A Case Report

종격동과 경부 림프절을 침범한 원발성 아밀로이드증: 증례 보고

  • Mun, Sung-Hee (Department of Radiology, School of Medicine, Catholic University of Daegu) ;
  • Jung, Kyung-Jae (Department of Radiology, School of Medicine, Catholic University of Daegu)
  • 문성희 (대구가톨릭대학교 의과대학 영상의학과학교실) ;
  • 정경재 (대구가톨릭대학교 의과대학 영상의학과학교실)
  • Published : 2011.08.01
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Abstract

Amyloidosis is a rare disease characterized by the accumulation of an insoluble protein called 'amyloid' in various soft tissues and organs. Primary localized amyloidosis involving the mediastinal and cervical lymph nodes is extremely rare. A 68-year-old man was hospitalized a few days ago for recent cerebral infarction and was diagnosed with primary localized amyloidosis manifesting as mediastinal and cervical lymphadenopathy with calcification. In this review, we report a case of primary localized amyloidosis involving the mediastinal and cervical lymph nodes along with its computed tomography findings. Amyloidosis should be considered as part of the differential diagnosis when the lymph nodes show low central attenuation and various types of calcification.

아밀로이드증은 아밀로이드가 다양한 조직과 장기에 침착되는 드문 질환으로 그 중에서도 종격동과 두경부 림프절을 침범하는 국소성 형태는 매우 드물다. 뇌경색으로 입원한 68세 남자 환자가 경부와 종격동의 석회화를 동반한 림프절 종대를 보인 림프절 아밀로이드증으로 진단되었다. 두경부 및 종격동 림프절 종대가 있으며 내부 저음영 부위와 다양한 석회화를 보일 때 감별진단에 포함되어야 할 아밀로이드증의 증례를 CT소견과 함께 보고한다.

Keywords

References

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