The CT and MR Imaging Findings of Adulthood Sinonasal Alveolar Rhabdomyosarcoma with Disseminated Metastases on $^{18}F$-FDG PET/CT: Report of Two Cases

미만성 전이를 보인 성인 비부비동 폐포형 횡문근육종의 $^{18}F$-FDG PET/CT, CT 및 MR 영상소견: 2예 보고

  • Bahn, Young-Eun (Department of Radiology, Dongsan Medical Center, Keimyung University School of Medicine) ;
  • Lee, Sang-Kwon (Department of Radiology, Dongsan Medical Center, Keimyung University School of Medicine)
  • 반영은 (계명대학교 의과대학 동산의료원 영상의학과) ;
  • 이상권 (계명대학교 의과대학 동산의료원 영상의학과)
  • Published : 2011.02.01

Abstract

We report herein two cases of adulthood sinonasal alveolar rhabdomyosarcoma that showed intense hypermetabolism and disseminated metastasis on $^{18}F$-FDG PET/CT. The contrast-enhanced CT (CECT) and gadolinium-enhanced T1-weighted images(Gd-T1WI) showed multiple rings of intense enhancement (the "botryoid sign") of the mass. Adulthood rhabdomyosarcoma should be considered when a sinonasal massshows the "botryoid sign" on CECT or Gd-T1WI, and intense hypermetabolism with disseminated metastases on 18F-FDG PET/CT.

저자들은 $^{18}F$-FDG PET/CT에서 강한 대사활성도와 미만성 전이를 보였던 성인에서 발병한 비부비동 폐포형 횡문근육종 2예를 보고하고자 한다. 이들 종양들은 조영증강 후 CT 및 T1-강조영상에서 포도송이 모양의 테두리형 조영증강을 보였다("botryoid sign"). 비부비동 종괴가 조영증강 후 CT 및 T1-강조영상에서 "botryoid sign"을 보이며, $^{18}F$-FDG PET/CT에서 강한 대사활성도 및 미만성 전이를 동반할 경우 성인에서 발병한 횡문근육종을 고려하여야 한다.

Keywords

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