The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
권호 표지

A Case of Pneumatosis Intestinalis in Refractory Acute Precursor B-Cell Lymphoblastic Leukemia-Lymphoma

불응성 급성전구B림프모세포백혈병 환자에서 발생한 장기종 1예

  • Bae, Suk-Hyang (Department of Internal Medicine, Dong-A University College of Medicine) ;
  • Hwang, Jin-Yeon (Department of Internal Medicine, Dong-A University College of Medicine) ;
  • Kim, Dong-Kyun (Department of Internal Medicine, Dong-A University College of Medicine) ;
  • Kim, Min-Sik (Department of Internal Medicine, Dong-A University College of Medicine) ;
  • Kwon, Hee-Jin (Department of Radiolgy, Dong-A University College of Medicine) ;
  • Han, Jin-Yeong (Department of Laboratory, Dong-A University College of Medicine) ;
  • Kim, Sung-Hyun (Department of Internal Medicine, Dong-A University College of Medicine)
  • 배숙향 (동아대학교 의과대학 내과학교실) ;
  • 황진연 (동아대학교 의과대학 내과학교실) ;
  • 김동균 (동아대학교 의과대학 내과학교실) ;
  • 김민식 (동아대학교 의과대학 내과학교실) ;
  • 권희진 (동아대학교 의과대학 진단방사선과학교실) ;
  • 한진영 (동아대학교 의과대학 진단검사의학교실) ;
  • 김성현 (동아대학교 의과대학 내과학교실)
  • Published : 2011.04.01
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Abstract

Pneumatosis intestinalis (PI) is an imaging phenomenon that represents air in the bowel wall. The cause of PI is variable, although specific etiologic factors remain unknown. It is an infrequent complication in leukemia patients and is associated with several medical and surgical conditions. PI often represents a benign condition, but it can also require surgery. Therefore, the assessment of PI with or without complications can be difficult. Herein, we report on an unusual case of a 63 year-old woman with refractory acute precursor B-cell lymphoblastic leukemia-lymphoma who presented with PI resulting from the leukemic process, and finally expired due to sepsis.

장기종은 소화기 장벽내 공기가 축적되는 방사선학적 소견이다. 장기종의 원인은 매우 다양하여 그 원인이 아직 명확하지 않다. 백혈병 환자에서 장기종은 약물치료 및 수술적 치료가 필요한 드문 합병증이다. 대부분의 장기종은 경과 및 예후가 좋은 편이지만 응급수술이 필요한 경우도 있으므로 치료 결정이 어려울 때가 많다. 저자들은 불응성 급성전구B 림프모세포백혈병 환자에서 백혈병의 진행과정으로서 장기종이 발생하여 결국 패혈증으로 사망한 증례를 경험하여 보고하는 바이다.

Keywords

References

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