The Korean Journal of Medicine

The Korean Association of Internal Medicine (대한내과학회)
권호 표지

A Case of Intrahepatic Sarcomatoid Cholangiocarcinoma with Rhabdoid Transformation

횡문근양 변형을 가지는 간내 육종양 담관암 1예

  • Kim, Wan-Soo (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Kim, Tae-Hyo (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Hwang, Jae-Jin (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Kim, Hyun-Jin (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Jung, Woon-Tae (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Lee, Ok-Jae (Department of Internal Medicine and Institute of Health Science, Gyeongsang National University School of Medicine) ;
  • Lee, Jeoung-Hee (Department of Pathology, Gyeongsang National University School of Medicine)
  • 김완수 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 김태효 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 황재진 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 김현진 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 정운태 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 이옥재 (경상대학교 의학전문대학원 내과학교실, 건강과학연구원) ;
  • 이정희 (경상대학교 의학전문대학원 병리과학교실)
  • Published : 2011.04.01
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Abstract

Rhabdoid transformation is an extremely rare occurrence in sarcomatoid cholangiocarcinoma. Only two cases have been reported in the medical literature worldwide, and its clinical and pathological characteristics remain unknown. Published case reports indicate that rhabdoid cholangiocarcinoma grows rapidly, with early metastasis and a particularly poor prognosis. Here, we report a case of rhabdoid transformation in sarcomatoid cholangiocarcinoma that exhibited aggressive behavior and resulted in a devastating prognosis.

간내 육종양 담관암은 원발성 간암 중 매우 드물게 발생하고, 이 중에서도 횡문근양 변형을 가지는 간내담관암은 보고된 예가 거의 없다. 간내 육종양 담관암은 매우 높은 침습성과 전이로 일반적인 선암에 비해 예후가 나쁜 종양으로 알려져 있다. 이에 저자들은 우상복부 동통으로 내원하여 내원 당시 이미 광범위한 국소 및 원격 전이가 있었고, 종양혈전에 의한 급성 뇌경색증의 합병증으로 불량한 예후를 보인 횡문근양 변형을 가지는 간내 육종양 담관암 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다.

Keywords

References

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