Journal of Cardiovascular Imaging

Korean Society of Echocardiography (한국심초음파학회)
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SPONTANEOUSLY HEALED MEMBRANOUS TYPE VENTRICULAR SEPTAL DEFECT WITH MALALIGNED INTERVENTRICULAR SEPTAL WALL AND DOUBLE-CHAMBERED RIGHT VENTRICLE IN A 56-YEAR-OLD PATIENT

  • Cho, Jung-Sun (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Youn, Ho-Joong (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Her, Sung-Ho (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Ahn, Soe-Hee (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Park, Mahn-Won (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Choi, Min-Suk (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Lee, Jae-Bum (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Baeg, Jeong-U (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Park, Chan-Seok (Department of Internal Medicine, School of Medicine, The Catholic University of Korea) ;
  • Kim, Mi-Jeong (Department of Internal Medicine, School of Medicine, The Catholic University of Korea)
  • Published : 2011.09.27
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Abstract

A 56-year-old male presented with resting dyspnea and chest discomfort for several years. During transthoracic and transesophageal echocardiography, a spontaneously healed membranous type ventricular septal defect (VSD) with malaligned interventricular septal wall, aneurysmal changes, a subaortic ridge and a double-chambered right ventricle (DCRV) was observed. When combined with DCRV, VSD with malalignment between the outlet and trabecular septa was associated with tetralogy of Fallot. The subaortic ridge was due to turbulent flow caused by the malalignment-type VSD. The VSD with malaligned interventricular septal wall can be developed after aneurismal changes of a perimembranous VSD. We report here in the unusual case of a 56-year-old patient who had a pathology complex comprising DCRV, subaortic ridge, spontaneously healed membranous type VSD with malaligned interventricular septal wall, and survived with surgical treatment.

Keywords

References

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