Korean Journal of Radiology

  • 제12권2호
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  • Pages.261-265
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  • 2011
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  • 1229-6929(pISSN)
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  • 2005-8330(eISSN)
대한영상의학회 (The Korean Society of Radiology)
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CT and MR Imaging Findings of Lymphangioleiomyomatosis Involving the Uterus and Pelvic Cavity

  • Kim, You-Sung (Department of Radiology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea) ;
  • Rha, Sung-Eun (Department of Radiology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea) ;
  • Byun, Jae-Young (Department of Radiology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea) ;
  • Lee, Ah-Won (Department of Hospital Pathology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea) ;
  • Park, Jong-Sup (Department of Obstetrics and Gynecology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea)
  • 발행 : 2011.04.01
⟨ 이전 논문 다음 논문 ⟩

초록

Lymphangioleiomyomatosis (LAM) is a rare idiopathic disease and this is characterized by a proliferation of abnormal smooth muscle cells in the lungs and in the lymphatic system of the thorax and retroperitoneum. The female genital tract is rarely affected by LAM. We report here on the CT and MR imaging findings of extensive LAM involving the uterus and pelvic cavity, and this was seen as multiple cystic uterine and parauterine masses with internal hemorrhage in a young female with tuberous sclerosis complex.

키워드

참고문헌

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피인용 문헌

  1. MR findings of uterine PEComa in patients with tuberous sclerosis: report of two cases vol.44, pp.4, 2019, https://doi.org/10.1007/s00261-019-01918-3
  2. Perivascular epithelioid cell tumors (PEComa) of the gynecologic tract vol.60, pp.3, 2021, https://doi.org/10.1002/gcc.22908