류마티스성 승모판 협착에 동반된 Levoatriocardinal 정맥을 통한 부분 폐정맥 환류 이상-자기공명영상 소견 및 성공적인 수술적 치료: 증례 보고

Partial Anomalous Pulmonary Venous Return via a Levoatriocardinal Vein in Association with Rheumatic Mitral Stenosis: MR Demonstration and Successful Surgical Repair

  • 현동호 (울산의대 서울아산병원 영상의학과) ;
  • 채은진 (울산의대 서울아산병원 영상의학과) ;
  • 서준범 (울산의대 서울아산병원 영상의학과) ;
  • 강준원 (울산의대 서울아산병원 영상의학과) ;
  • 도경현 (울산의대 서울아산병원 영상의학과) ;
  • 이충욱 (울산의대 서울아산병원 영상의학과) ;
  • 이현주 (울산의대 서울아산병원 영상의학과) ;
  • 황혜전 (울산의대 서울아산병원 영상의학과) ;
  • 임태환 (울산의대 서울아산병원 영상의학과)
  • Hyun, Dong-Ho (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Chae, Eun-Jin (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Seo, Joon-Beom (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Kang, Joon-Won (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Do, Kyung-Hyun (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Choong-Wook (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lee, Hyun-Joo (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Hwang, Hye-Jeon (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine) ;
  • Lim, Tae-Hwan (Department of Radiology and Research Institute of Radiology, Asan Medical Center, University of Ulsan College of Medicine)
  • 투고 : 2010.04.12
  • 심사 : 2010.06.20
  • 발행 : 2010.10.01

초록

류마티스성 승모판 협착에 부분 폐정맥 환류 이상이 합병된 증례는 드물게 보고되고 있으며 이런 경우 부분 폐정맥 환류 이상의 합병으로 인한 혈류 역학적 변화를 수술 전에 평가하는 것이 적절한 치료를 위해서 필수적이다. 저자들은 류마티스성 승모판 협착에 levoatriocardinal 정맥을 통한 부분 폐정맥 환류 이상이 합병된 환자에서 수술 전전산화단층촬영과 자기공명영상을 통해 levoatriocardinal 정맥을 진단하고 부분 폐정맥 환류 이상에 의한 혈류역학적 변화를 정량적으로 평가함으로써 성공적인 수술적 치료가 가능했던 증례를 보고하고자 한다.

The preoperative evaluation of the hemodynamics associated with PAPVR and rheumatic mitral valve stenosis is necessary for successful surgical treatment, even though the incidence rate is rare. The purpose of this case report is to present the usefulness of CT and MRI for diagnosing rheumatic mitral stenosis and partial anomalous pulmonary venous connection to the left innominate vein accompanied by the presence of the levoatriocardinal vein and evaluating its flow dynamics.

키워드

참고문헌

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