A case of primary small cell neuroendocrine carcinoma of the liver

원발성 간 소세포암 1예

  • Yoon, June-Young (Department of Internal Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Chung, Hyoung-Jung (Department of Internal Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Choi, Hye-Young (Department of Internal Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Choi, Jong-Su (Department of Internal Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Eom, Dae-Woon (Department of Pathology, Gangneung Asan Hospital, University of Ulsan College of Medicine) ;
  • Oh, Ho-Suk (Department of Internal Medicine, Gangneung Asan Hospital, University of Ulsan College of Medicine)
  • 윤준영 (울산대학교 의과대학 강릉아산병원 내과학교실) ;
  • 정형정 (울산대학교 의과대학 강릉아산병원 내과학교실) ;
  • 최혜영 (울산대학교 의과대학 강릉아산병원 내과학교실) ;
  • 최종수 (울산대학교 의과대학 강릉아산병원 내과학교실) ;
  • 엄대운 (울산대학교 의과대학 강릉아산병원 병리과학교실) ;
  • 오호석 (울산대학교 의과대학 강릉아산병원 내과학교실)
  • Received : 2008.02.27
  • Accepted : 2008.07.28
  • Published : 2010.07.01

Abstract

Extrapulmonary small cell carcinoma is a highly malignant and poorly differentiated neuroendocrine tumor. The overall incidence in the United States is approximately 0.1~0.4%. Moreover, small cell carcinoma of the liver is extremely rare and few cases have been reported in the literature. We experienced a 65-year-old woman with a 15 cm hepatic mass, which was localized in the left lobe of a noncirrhotic liver. The mass was confirmed as small cell carcinoma by immunohistochemical staining of a biopsy specimen. Other possible primary sites were excluded by radiologic and endoscopic evaluations. The patient was treated with combination chemotherapy. She was in partial response on the last follow-up visit.

Keywords

References

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