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Synovial Sarcoma Arising from the Chest Wall in a Child

소아의 흉벽에서 발생한 윤활막 육종

  • Kim, Seok (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Catholic University of Daegu) ;
  • Park, Ki-Sung (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Catholic University of Daegu) ;
  • Bae, Chi-Hoon (Department of Thoracic and Cardiovascular Surgery, School of Medicine, Catholic University of Daegu)
  • 김석 (대구가톨릭대학교 의과대학 흉부외과학교실) ;
  • 박기성 (대구가톨릭대학교 의과대학 흉부외과학교실) ;
  • 배지훈 (대구가톨릭대학교 의과대학 흉부외과학교실)
  • Received : 2010.01.21
  • Accepted : 2010.02.16
  • Published : 2010.08.05

Abstract

Synovial sarcoma is a malignant soft-tissue tumor that most commonly occurs in the extremities of young adults. There have been several cases of synovial sarcomas of the pleural and lung reported, but synovial sarcoma arising from the chest wall in childhood is very rare. Here we report a case of synovial sarcoma arising from the chest wall in a 3 year-old female patient. The tumor was completely resected. No adjuvant therapy was given. The patient is well 3 years after the operation.

윤활막육종은 젊은 성인의 팔, 다리에 호발하는 악성종양이다. 흉막, 폐에 발생하는 윤활막육종은 드물게 보고되고 있으나, 본 증례처럼 흉벽에 생기면서 소아에 발생한 경우는 매우 드물다. 저자들은 소아의 흉벽에 발생한 윤활막종을 수술 치료한 경험을 보고하는 바이다. 현재 환아는 술 후 3년 동안 재발없이 잘 지내고 있는 중이다.

Keywords

References

  1. Wright PH, Sim FH, Soule EH, Taylor WF. Synovial sarcoma. J Bone Joint Surg Am 1982;64:112-22. https://doi.org/10.2106/00004623-198264010-00016
  2. Duran.Mendicuti A, Costello P, Vargas SO. Primary synovial sarcoma of the chest: radiographic and clinicopathologic correlation. J Thorac Imaging 2003;18:87-93. https://doi.org/10.1097/00005382-200304000-00006
  3. Hung JJ, Chou TY, Sun CH, Liu JS, Hsu WH. Primary synovial sarcoma of the posterior chest wall. Ann Thorac Surg 2008;85:2120-2. https://doi.org/10.1016/j.athoracsur.2008.01.004
  4. Bui-Mansfield LT, Kaplan KJ, Boardman J. Radiologicpathologic conference of keller army community hospital at west point, the united states military academy: synovial sarcoma of the chest wall. Am J Roentgenol 2002;179:880. https://doi.org/10.2214/ajr.179.4.1790880
  5. Nicholson AG, Goldstraw P, Fisher C. Synovial sarcoma of the pleura and its differentiation from other primary pleural tumors: a clinicopathologic and immunohistochemical review of three cases. Histopathology 1998;33:508-13. https://doi.org/10.1046/j.1365-2559.1998.00565.x
  6. Frazier AA, Franks TJ, Pugatch RD, Galvin JR. From the archives of the AFIP: pleuropulmonary synovial sarcoma. Radiographics 2006;26:923-40. https://doi.org/10.1148/rg.263055211
  7. Lewis JJ, Antonescu CR, Leung DHY, et al. Synovial sarcoma: a multivariate analysis of prognostic factors in 112 patients with primary localized tumors of the extremity. J Clin Oncol 2000;18:2087-94.
  8. Wolden SL. Radiation therapy for non-rhabdomyosarcoma soft tissue sarcomas in adolescents and young adults. J Pediatr Hematol Oncol 2005;27:212-4. https://doi.org/10.1097/01.mph.0000161763.53175.ad