Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
권호 표지
DOI QR코드

DOI QR Code

Spontaneous Pneumothorax due to Pulmonary Invasion in Multisystemic Langerhans Cell Histiocytosis

다체계 랑거한스 세포 조직구 증식증에 의해 발생한 기흉

  • Cho, Kyu-Seok (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University) ;
  • Kim, Jung-heon (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University) ;
  • Youn, Hyo-Chul (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University) ;
  • Kim, Soo-Cheol (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University) ;
  • Kim, Bum-Shik (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University) ;
  • Park, Joo-Chul (Department of Thoracic and Cardiovascular Surgery, College of Medicine, Kyung Hee University)
  • 조규석 (경희대학교 의과대학 흉부외과학교실) ;
  • 김중헌 (경희대학교 의과대학 흉부외과학교실) ;
  • 윤효철 (경희대학교 의과대학 흉부외과학교실) ;
  • 김수철 (경희대학교 의과대학 흉부외과학교실) ;
  • 김범식 (경희대학교 의과대학 흉부외과학교실) ;
  • 박주철 (경희대학교 의과대학 흉부외과학교실)
  • Received : 2009.10.01
  • Accepted : 2010.06.08
  • Published : 2010.08.05
Download PDF
⟨ Previous Next ⟩

Abstract

Langerhans cell Histiocytosis can present as a single or multiple lesion and can affect one or several organ systems. A 41-year-old woman with a history of multisystemic Langerhans cell Histiocytosis invading lung and thyroid was admitted with left-sided spontaneous pneumothorax. Here we report a case of uncommon pulmonary Langerhans-cell Histiocytosis presenting with spontaneous pneumothorax as a multisystemic Langerhans cell Histiocytosis.

랑거한스 세포 조직구 증식증이 2개 이상의 장기를 침범하게 되면 다체계 병변이라고 한다. 폐와 갑성선을 침범한 다체계 랑거한스 조직구 증식증을 진단 받은 41세 여자 환자에서 기흉의 형태로 발현 되어진 다체계 랑거한스 조직구 증식증의 치료 경험을 보고 하는 바이다.

Keywords

References

  1. Robert V, Jay HR, Darrell RS, Paul AD, Andrew HL. Clinical outcomes of pulmonary Langerhans-cell histiocytosis in adults, N Engl J Med 2002;346:484-90. https://doi.org/10.1056/NEJMoa012087
  2. Favara BE, Feller AC, Pauli M, et al. Contemporary classification of histiocytic disorders. Med Pediatr Oncol 1996;9: 157-66.
  3. Vassilios ND, Grigoris lB, Dimitrios AM, Georgios lB. Pulmonary invasion in multisystem Langerhans cell histiocytosis. Ann Thorac Surg 2003;75:1656. https://doi.org/10.1016/S0003-4975(02)04174-7
  4. Vasallo R, Ryu JH, Colby TV, et al. Pulmonary Langerhans- cell histiocytosis. N Eng J Med 2000;342:1969-78. https://doi.org/10.1056/NEJM200006293422607
  5. Krawczykk P, Kieszkor, Siwiec J, Milanowski J. Difficulties in the diagnosis of rare immunological diseases manifesting with cystic Iung diseases and spontaneous pneumothorax, case reports. Heart Lung 2004;33:21-5. https://doi.org/10.1016/j.hrtlng.2003.10.005
  6. Delobbe A, Euricu J, Duhamel A, Wallaert B. Determinants of survival in pulmonary Langerhans cell granulomatosis. Eur Respir J 1996;9:2002-6. https://doi.org/10.1183/09031936.96.09102002
  7. Rami B, Schneider U, Wandl-Vergesslich K, Frisch H, Schober A. Primary hypothyroidism, central diabetes inspidus and growth hormone deficiency in multisystem Langer hans cell histiocytosis; a case report. Acta Pediatr 1998;87: 112-4. https://doi.org/10.1111/j.1651-2227.1998.tb01400.x
  8. Sin SY, Kim KN, Lee SY. A case of pulmonary Langerhans cell Histiocytosis with pneumothrax. J Korean Acad Fam Med 2005;26:346-9.
  9. Yoo BS, Lee JW, Jo TJ, ct al. A case of pulmonary Langerhans cell histiocytosis associated with central diabetes insipidus in adult. Korean J Thorac Cardiovasc Surg 2005; 38:866-9.