A Case of Giant Sacral Chordoma

천추부에 발생한 거대 척색종 치험 1례

  • Suh, Bum-Sin (Departments of Plastic and Reconstructive Surgery, School of Medicine, Wonkwang University) ;
  • Na, Young-Cheon (Departments of Plastic and Reconstructive Surgery, School of Medicine, Wonkwang University) ;
  • Park, Jong-Tae (Departments of Neurosurgery, School of Medicine, Wonkwang University)
  • 서범신 (원광대학교 의과대학 성형외과학교실) ;
  • 나영천 (원광대학교 의과대학 성형외과학교실) ;
  • 박종태 (원광대학교 의과대학 신경외과학교실)
  • Received : 2010.04.15
  • Accepted : 2010.06.14
  • Published : 2010.09.10

Abstract

Purpose: Chordoma is a rare primary osseous tumor arising from the remnants of the primitive notochord. It occurs once in 2,000,000. It is characterized by its slow growth, high frequency to invade destroy bone by direct extension. We experienced giant sacral chordoma and reconstructed with gluteal advancement flap. Methods: A 52-year-old woman presented with a 2-years history of gluteal pain. In the biopsy study revealed sacral chordoma. MRI study showed $13{\times}12{\times}10\;cm$ sized m0cs. We approached anterior and posterior resection and reconstructed with bilateral gluteus maximus advancement flap. Results: After the operation, blader and anal function were slightly decreased. But, 4 months later those were almost fully recovered. There was no significant complication and recurrence after 2-years follow-up. Conclusion: Chordoma is characterized by its slow growth, high frequency to invade and destroy bone by direct extension. Wide surgical resection is the only curative procedure. We report a ase of giant sacral chordoma which was successfully treated by anterior and posterior approach and reconstructed with bilateral gluteal advancement flap.

Keywords

References

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