Clinical and Experimental Pediatrics

대한소아청소년과학회 (The Korean Pediatric Society)
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Perivascular epithelioid cell tumor (PEComa) of the ascending colon: the implication of IFN-${\alpha}$ 2b treatment

  • Park, Sun-Ju (Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Han, Dong-Kyun (Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Baek, Hee-Jo (Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Chung, Sang-Young (Department of Pediatric Surgery, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Nam, Jong-Hee (Department of Pathology, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Kook, Hoon (Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School) ;
  • Hwang, Tai-Ju (Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School)
  • 투고 : 2010.03.04
  • 심사 : 2010.09.13
  • 발행 : 2010.11.15
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초록

A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PEComa). PEComa in the colon is very rare. Only a few cases have been reported so far. An effective treatment method for this rare tumor has not been established yet. The patient received adjuvant interferon-${\alpha}$ immunotherapy for 1 year. He has been tumor-free for 26 months since the initial diagnosis. This report is the first documented case of the use of interferon-${\alpha}$ for pediatric PEComa of the colon.

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참고문헌

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피인용 문헌

  1. A Case of a Perivascular Epithelioid Cell Tumor Mimicking Colon Cancer vol.60, pp.6, 2010, https://doi.org/10.4166/kjg.2012.60.6.377
  2. Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature vol.12, pp.None, 2014, https://doi.org/10.1186/1477-7819-12-12
  3. Malignant Perivascular Epithelioid Cell Tumor of the Gallbladder: A Case Report and Review of Literature vol.138, pp.9, 2014, https://doi.org/10.5858/arpa.2013-0092-cr
  4. Perivascular Epithelioid Cell Tumor of Gastrointestinal Tract : Case Report and Review of the Literature vol.94, pp.3, 2010, https://doi.org/10.1097/md.0000000000000393
  5. A systematic review: perivascular epithelioid cell tumor of gastrointestinal tract vol.95, pp.28, 2016, https://doi.org/10.1097/md.0000000000003890
  6. A Liver Transplant for Local Control in a Pediatric Patient with Metastatic TFE3-Associated Perivascular Epithelioid Cell Tumor (PEComa) to the Liver vol.2021, pp.None, 2021, https://doi.org/10.1155/2021/3924565
  7. PEComa in the rectum: A case report and review of the literature on epithelioid angiomyolipoma vol.86, pp.None, 2010, https://doi.org/10.1016/j.ijscr.2021.106301
  8. Unusual paediatric sigmoid perivascular epithelioid cell tumour with regional lymph node metastasis treated using gemcitabine and docetaxel: a case report and literature review vol.49, pp.9, 2010, https://doi.org/10.1177/03000605211041509