Investigative Magnetic Resonance Imaging

Korean Society of Magnetic Resonance in Medicine (대한자기공명의과학회)
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Non-Functioning, Malignant Pancreatic Neuroendocrine Tumor in a 16-Year-old Boy: A Case Report

16세 남아에서 발생한 췌장의 비기능성 악성 신경내분비 종양: 증례 보고

  • Lim, Se-Woong (Department of Radiology, Wonkwang University School of Medicine and Hospital) ;
  • Lee, Young-Hwan (Department of Radiology, Wonkwang University School of Medicine and Hospital) ;
  • Choi, See-Sung (Department of Radiology, Wonkwang University School of Medicine and Hospital) ;
  • Cho, Hyun-Sun (Department of Radiology, Inje University Sanggyepaik Hospital)
  • 임세웅 (원광대학교 의과대학 영상의학과) ;
  • 이영환 (원광대학교 의과대학 영상의학과) ;
  • 최시성 (원광대학교 의과대학 영상의학과) ;
  • 조현선 (인제대학교 상계백병원 영상의학과)
  • Received : 2010.09.14
  • Accepted : 2010.10.19
  • Published : 2010.12.30
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Abstract

We report the case of a 16-year-old boy with a solid pancreatic mass which proved to be a nonfunctioning, malignant pancreatic neuroendocrine tumor (PNET). In pediatric patients, malignant pancreatic tumors are rare, especially malignant PNET. When dynamic contrast enhanced MRI showed a well enhancing solid pancreatic tumor on arterial and delayed phases and combined with malignant features, such as vascular invasion, invasion of adjascent organs, and lymphadenopathy, we should include malignant pancreatic neuroendocrine tumor in the differential diagnosis of childhood pancreatic tumors.

소아에서 췌장의 악성 종양은 매우 드물게 발생하고 있으며, 특히 악성 신경내분비 종양은 더더욱 드물다. 저자들은 16세 소아 환자에서 발생한 비기능성 악성 신경내분비 종양의 증례를 경험하여 CT와 MRI 소견을 보고하고자 한다. 췌장 두부에서 발생한 고형 종양으로 조영증강 MRI의 문맥기에서 지연기로 갈수록 조영증강이 잘 되고, 주변의 혈관 침습, 총담관 폐색, 림프절병증 등 악성 소견을 동반할 때 췌장의 비기능성 악성 신경내분비 종양을 감별 진단에 포함하여야 한다.

Keywords

References

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