Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Surgical Treatment of Dermatofibrosarcoma Protuberans of the Chest Wall

흉벽의 융기피부섬유육종의 수술적 치료

  • Cho, Hyun-Min (Department of Thoracic and Cardiovascular Surgery, Konyang University Hospital) ;
  • Kim, Young-Jin (Department of Thoracic and Cardiovascular Surgery, Konyang University Hospital) ;
  • Lee, Tae-Yeon (Department of Thoracic and Cardiovascular Surgery, Konyang University Hospital) ;
  • Lee, Chan-Kyu (Department of Thoracic and Cardiovascular Surgery, Konyang University Hospital) ;
  • Seok, June-Pill (Department of Thoracic and Cardiovascular Surgery, Konyang University Hospital) ;
  • Lee, Yong-Hae (Department of Plastic Surgery, Konyang University Hospital)
  • 조현민 (건양대학교병원 흉부외과) ;
  • 김영진 (건양대학교병원 흉부외과) ;
  • 이태연 (건양대학교병원 흉부외과) ;
  • 이찬규 (건양대학교병원 흉부외과) ;
  • 석준필 (건양대학교병원 흉부외과) ;
  • 이용해 (건양대학교병원 성형외과)
  • Received : 2010.09.30
  • Accepted : 2010.11.15
  • Published : 2010.12.05
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Abstract

A 77-year-old man presented with a huge protruding mass on the left anterior chest wall. The tumor was resected and diagnosed as dermatofibrosarcoma protuberans (DFSP). DFSP is an uncommon, intermediate-grade mesenchymal cutaneous tumor which extends deep into subcutaneous tissue and may invade through the fascial planes and into muscle but rarely metastasize. Histologically, DFSP is composed of spindle cells arranged in an irregularly whorled or storiform pattern. The histological diagnosis can be confirmed with immunohistochemical staining for CD34. We report a case of DFSP. The tumor was completely excised and the chest wall was reconstructed using latissimus dorsi muscle flap and skin graft.

77세 남자 환자가 좌측 전흉벽의 거대한 종괴를 주소로 내원하였으며 수술적 제거 후 융기피부섬유 육종으로 진단되었다. 융기피부섬유육종은 피부의 중간엽 종양으로 연조직 육종의 2% 미만을 차지하며 병변은 진피에서 기원하여 피하조직까지 침범 할 수 있는 종양이다. 조직학적으로 방추세포의 나선형 배열이 특징적이며 CD34의 면역조직 화학 특수 염색에서 양성소견을 보인다. 저자들은 광범위 절제술과 전층피부이식을 통한 흉부재건술로 거대한 흉부 융기피부섬유육종을 성공적으로 절제하였기에 보고하는 바이다.

Keywords

References

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